KAT6B Chromosome 10

Lysine acetyltransferase 6B
262 variants 262 Health Risk

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What This Gene Does
The protein encoded by this gene is a histone acetyltransferase and component of the MOZ/MORF protein complex. In addition to its acetyltransferase activity, the encoded protein has transcriptional activation activity in its N-terminal end and transcriptional repression activity in its C-terminal end. This protein is necessary for RUNX2-dependent transcriptional activation and could be involved in brain development. Mutations have been found in patients with genitopatellar syndrome. A translocation of this gene and the CREBBP gene results in acute myeloid leukemias. Three transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Mar 2012]
Gene Info
Gene Group
"PHD finger proteins|MYST type domain containing lysine acetyltransferases|Zinc fingers MYST C2HC-type"
Locus Type
gene with protein product
Location
10q22.2
Ensembl
ENSG00000156650
Associated Conditions (37)
Genitopatellar syndrome
Blepharophimosis - intellectual disability syndrome
SBBYS type
Inborn genetic diseases
Autosomal dominant KAT6B-related disorders
KAT6B-related disorder
9 conditions
Intellectual disability
Developmental disorder
KAT6B-related multiple congenital anomalies syndrome
Left ventricular noncompaction
Hypospadias
Seizure
Macrocephaly
Generalized joint hypermobility
Joint laxity
Delayed speech and language development
Hepatocellular carcinoma
10 conditions
Chromatinopathy
+17 more conditions
Key Variants
RS1014954135
Conflicting classifications of pathogenicity
Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
Health Risk
RS1019373559
Conflicting classifications of pathogenicity
Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
Health Risk
RS1054836015
Conflicting classifications of pathogenicity
Blepharophimosis - intellectual disability syndrome, SBBYS type, Genitopatellar syndrome
Health Risk
RS1057520090
Conflicting classifications of pathogenicity
Genitopatellar syndrome, Genitopatellar syndrome
Health Risk
RS11001247
Conflicting classifications of pathogenicity
Genitopatellar syndrome, Genitopatellar syndrome
Health Risk
RS113566014
Conflicting classifications of pathogenicity
Inborn genetic diseases, Genitopatellar syndrome, Inborn genetic diseases
Health Risk
RS1167009272
Conflicting classifications of pathogenicity
Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
Health Risk
RS1213787718
Conflicting classifications of pathogenicity
Genitopatellar syndrome, Genitopatellar syndrome
Health Risk
RS1222902525
Conflicting classifications of pathogenicity
Genitopatellar syndrome, Genitopatellar syndrome
Health Risk
RS1265658401
Conflicting classifications of pathogenicity
Genitopatellar syndrome, Inborn genetic diseases, Genitopatellar syndrome
Health Risk
RS1273966358
Conflicting classifications of pathogenicity
Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
Health Risk
RS1274585455
Conflicting classifications of pathogenicity
Genitopatellar syndrome, Inborn genetic diseases, Genitopatellar syndrome
Health Risk
All Variants (262)
RSID Category Clinical Significance Conditions
RS1014954135 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS1019373559 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS1054836015 Health Risk Conflicting classifications of pathogenicity Blepharophimosis - intellectual disability syndrome, SBBYS type, Genitopatellar syndrome
RS1057520090 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS11001247 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS113566014 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Genitopatellar syndrome, Inborn genetic diseases
RS1167009272 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS1213787718 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS1222902525 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS1265658401 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Inborn genetic diseases, Genitopatellar syndrome
RS1273966358 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS1274585455 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Inborn genetic diseases, Genitopatellar syndrome
RS1281390253 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS1287506606 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS1305986308 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS1315521603 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS1351645436 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS1367725176 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS138030591 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS1383727273 Health Risk Conflicting classifications of pathogenicity Autosomal dominant KAT6B-related disorders, Genitopatellar syndrome, Autosomal dominant KAT6B-related disorders
RS138617006 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Genitopatellar syndrome, Inborn genetic diseases
RS1389265622 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS140989004 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS140992439 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS141200092 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS1415150379 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Genitopatellar syndrome, Inborn genetic diseases
RS1425905429 Health Risk Conflicting classifications of pathogenicity KAT6B-related disorder, Genitopatellar syndrome, KAT6B-related disorder
RS143090869 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS144976646 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS145636342 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Inborn genetic diseases, Genitopatellar syndrome
RS147168060 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, KAT6B-related disorder, Inborn genetic diseases
RS148243411 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Inborn genetic diseases, KAT6B-related disorder
RS149817329 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Genitopatellar syndrome, Inborn genetic diseases
RS1554846212 Health Risk Conflicting classifications of pathogenicity 9 conditions, 9 conditions
RS1564516087 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS1564626392 Health Risk Conflicting classifications of pathogenicity Intellectual disability, Intellectual disability
RS1564632292 Health Risk Conflicting classifications of pathogenicity Developmental disorder, KAT6B-related multiple congenital anomalies syndrome, Developmental disorder
RS182593735 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Inborn genetic diseases, Genitopatellar syndrome
RS184028635 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS1845383523 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS1845730108 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1846260900 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS187153114 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Inborn genetic diseases, Genitopatellar syndrome
RS199806711 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS200393557 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, KAT6B-related disorder, Inborn genetic diseases
RS201792033 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Genitopatellar syndrome
RS202037961 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Inborn genetic diseases, Genitopatellar syndrome
RS2134165271 Health Risk Conflicting classifications of pathogenicity Blepharophimosis - intellectual disability syndrome, SBBYS type, Blepharophimosis - intellectual disability syndrome
RS2134237417 Health Risk Conflicting classifications of pathogenicity Genitopatellar syndrome, Blepharophimosis - intellectual disability syndrome, SBBYS type
RS2134241318 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Genitopatellar syndrome, Inborn genetic diseases
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