IGF2 Chromosome 11

Insulin like growth factor 2
27 variants 27 Health Risk

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What This Gene Does
This gene encodes a member of the insulin family of polypeptide growth factors, which are involved in development and growth. It is an imprinted gene, expressed only from the paternal allele, and epigenetic changes at this locus are associated with Wilms tumour, Beckwith-Wiedemann syndrome, rhabdomyosarcoma, and Silver-Russell syndrome. A read-through INS-IGF2 gene exists, whose 5' region overlaps the INS gene and the 3' region overlaps this gene. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2010]
Gene Info
Gene Group
"MicroRNA protein coding host genes|Neuropeptides|Insulin family"
Locus Type
gene with protein product
Location
11p15.5
Ensembl
ENSG00000167244
Associated Conditions (8)
Inborn genetic diseases
Silver-Russell syndrome 3
Silver-Russell syndrome 1
Beckwith-Wiedemann syndrome
Wilms tumor 1
Colorectal cancer
IGF2-related disorder
See cases
Key Variants
All Variants (27)
RSID Category Clinical Significance Conditions
RS146334276 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS150866176 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Silver-Russell syndrome 3, Silver-Russell syndrome 1
RS200441006 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Beckwith-Wiedemann syndrome, Wilms tumor 1
RS554804044 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS764865819 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS868067982 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1057518115 Health Risk Likely pathogenic
RS142012621 Health Risk Likely pathogenic Inborn genetic diseases, Silver-Russell syndrome 3, Inborn genetic diseases
RS1858779370 Health Risk Likely pathogenic Silver-Russell syndrome 3, Silver-Russell syndrome 3
RS2133582387 Health Risk Likely pathogenic
RS2495572126 Health Risk Likely pathogenic Silver-Russell syndrome 3, Silver-Russell syndrome 3
RS2495576425 Health Risk Likely pathogenic Silver-Russell syndrome 3, Silver-Russell syndrome 3
RS2495590067 Health Risk Likely pathogenic Silver-Russell syndrome 3, Silver-Russell syndrome 3
RS1064794050 Health Risk Pathogenic Silver-Russell syndrome 1, Silver-Russell syndrome 1
RS1114167321 Health Risk Pathogenic Silver-Russell syndrome 1, Silver-Russell syndrome 1
RS1858717597 Health Risk Pathogenic Colorectal cancer, Colorectal cancer
RS1858932834 Health Risk Pathogenic Silver-Russell syndrome 3, Silver-Russell syndrome 3
RS1858936079 Health Risk Pathogenic Silver-Russell syndrome 3, Silver-Russell syndrome 3
RS1858937182 Health Risk Pathogenic Silver-Russell syndrome 3, Silver-Russell syndrome 3
RS1858937359 Health Risk Pathogenic Silver-Russell syndrome 3, Wilms tumor 1, Beckwith-Wiedemann syndrome
RS2495576486 Health Risk Pathogenic Silver-Russell syndrome 3, Silver-Russell syndrome 3
RS2495589617 Health Risk Pathogenic IGF2-related disorder, IGF2-related disorder
RS2495590166 Health Risk Pathogenic
RS2495591068 Health Risk Pathogenic Silver-Russell syndrome 3, Silver-Russell syndrome 3, Silver-Russell syndrome 3
RS553443857 Health Risk Pathogenic
RS869320620 Health Risk Pathogenic Silver-Russell syndrome 3, Silver-Russell syndrome 3
RS2495590055 Health Risk Pathogenic/Likely pathogenic See cases, See cases
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