IFNAR2 Chromosome 21

Interferon alpha and beta receptor subunit 2
18 variants 18 Health Risk

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What This Gene Does
The protein encoded by this gene is a type I membrane protein that forms one of the two chains of a receptor for interferons alpha and beta. Binding and activation of the receptor stimulates Janus protein kinases, which in turn phosphorylate several proteins, including STAT1 and STAT2. The protein belongs to the type II cytokine receptor family. Mutations in this gene are associated with Immunodeficiency 45. [provided by RefSeq, Jul 2020]
Gene Info
Gene Group
Interferon receptors
Locus Type
gene with protein product
Location
21q22.11
Ensembl
ENSG00000159110
Associated Conditions (9)
Hepatitis B virus
susceptibility to
Immunodeficiency 45
IFNAR2-related disorder
Susceptibility to severe COVID-19
Primary immunodeficiency with post-measles-mumps-rubella vaccine viral infection
Multisystem inflammatory syndrome in children
Mortality risk in patients with severe coronavirus disease (COVID-19)
Associated with severe COVID-19 disease
Key Variants
All Variants (18)
RSID Category Clinical Significance Conditions
RS140533677 Health Risk Conflicting classifications of pathogenicity Hepatitis B virus, susceptibility to, Immunodeficiency 45
RS150825310 Health Risk Conflicting classifications of pathogenicity Immunodeficiency 45, Immunodeficiency 45
RS1987287426 Health Risk Conflicting classifications of pathogenicity Immunodeficiency 45, Immunodeficiency 45
RS780171388 Health Risk Conflicting classifications of pathogenicity IFNAR2-related disorder, IFNAR2-related disorder
RS1468003457 Health Risk Likely pathogenic Immunodeficiency 45, Immunodeficiency 45
RS2123478681 Health Risk Likely pathogenic
RS903202071 Health Risk Likely pathogenic
RS774005366 Health Risk Likely risk allele Susceptibility to severe COVID-19, Susceptibility to severe COVID-19
RS1164631131 Health Risk Pathogenic
RS1205259499 Health Risk Pathogenic
RS1312285586 Health Risk Pathogenic Primary immunodeficiency with post-measles-mumps-rubella vaccine viral infection, Immunodeficiency 45, Primary immunodeficiency with post-measles-mumps-rubella vaccine viral infection
RS2516718524 Health Risk Pathogenic
RS761669332 Health Risk Pathogenic
RS775739391 Health Risk Pathogenic Immunodeficiency 45, Immunodeficiency 45
RS778657924 Health Risk Pathogenic
RS1310889473 Health Risk Pathogenic/Likely pathogenic Primary immunodeficiency with post-measles-mumps-rubella vaccine viral infection, Immunodeficiency 45, Primary immunodeficiency with post-measles-mumps-rubella vaccine viral infection
RS1226146327 Health Risk risk factor Multisystem inflammatory syndrome in children, Multisystem inflammatory syndrome in children
RS3153 Health Risk Uncertain significance; association Mortality risk in patients with severe coronavirus disease (COVID-19), Associated with severe COVID-19 disease, Mortality risk in patients with severe coronavirus disease (COVID-19)
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