HBB Chromosome 11

Hemoglobin subunit beta
398 variants 398 Health Risk

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What This Gene Does
The alpha (HBA) and beta (HBB) loci determine the structure of the 2 types of polypeptide chains in adult hemoglobin, Hb A. The normal adult hemoglobin tetramer consists of two alpha chains and two beta chains. Mutant beta globin causes sickle cell anemia. Absence of beta chain causes beta-zero-thalassemia. Reduced amounts of detectable beta globin causes beta-plus-thalassemia. The order of the genes in the beta-globin cluster is 5'-epsilon -- gamma-G -- gamma-A -- delta -- beta--3'. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Hemoglobin subunits
Locus Type
gene with protein product
Location
11p15.4
Ensembl
ENSG00000244734
Associated Conditions (181)
HEMOGLOBIN LA DESIRADE
Hb SS disease
Hemoglobinopathy
8 conditions
beta Thalassemia
Beta-thalassemia HBB/LCRB
HBB-related disorder
Fetal hemoglobin quantitative trait locus 1
Hemoglobin E
Inborn genetic diseases
HEMOGLOBIN PYRGOS
Malaria
susceptibility to
HEMOGLOBIN N (BALTIMORE)
HEMOGLOBIN N (JENKINS)
HEMOGLOBIN JENKINS
HEMOGLOBIN HOPKINS 1
HEMOGLOBIN KENWOOD
HEMOGLOBIN G (COPENHAGEN)
HEMOGLOBIN G (SASKATOON)
+161 more conditions
Key Variants
All Variants (398)
RSID Category Clinical Significance Conditions
RS1011427406 Health Risk Conflicting classifications of pathogenicity
RS1034207896 Health Risk Conflicting classifications of pathogenicity
RS111645889 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN LA DESIRADE, Hb SS disease, Hemoglobinopathy
RS111851677 Health Risk Conflicting classifications of pathogenicity beta Thalassemia, Beta-thalassemia HBB/LCRB, HBB-related disorder
RS113082294 Health Risk Conflicting classifications of pathogenicity beta Thalassemia, Fetal hemoglobin quantitative trait locus 1, Hb SS disease
RS1164871363 Health Risk Conflicting classifications of pathogenicity
RS1184042209 Health Risk Conflicting classifications of pathogenicity
RS1215164743 Health Risk Conflicting classifications of pathogenicity
RS1251286087 Health Risk Conflicting classifications of pathogenicity
RS1272414751 Health Risk Conflicting classifications of pathogenicity beta Thalassemia, beta Thalassemia
RS1291160651 Health Risk Conflicting classifications of pathogenicity
RS1334966870 Health Risk Conflicting classifications of pathogenicity
RS138405215 Health Risk Conflicting classifications of pathogenicity
RS1428777319 Health Risk Conflicting classifications of pathogenicity
RS145669504 Health Risk Conflicting classifications of pathogenicity beta Thalassemia, Hemoglobin E, Hb SS disease
RS1554918013 Health Risk Conflicting classifications of pathogenicity
RS1554918177 Health Risk Conflicting classifications of pathogenicity
RS1803195 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN PYRGOS, HEMOGLOBIN PYRGOS
RS1847534399 Health Risk Conflicting classifications of pathogenicity
RS1847534694 Health Risk Conflicting classifications of pathogenicity
RS1847536038 Health Risk Conflicting classifications of pathogenicity
RS1847537565 Health Risk Conflicting classifications of pathogenicity
RS185607297 Health Risk Conflicting classifications of pathogenicity beta Thalassemia, beta Thalassemia
RS191535077 Health Risk Conflicting classifications of pathogenicity
RS193922558 Health Risk Conflicting classifications of pathogenicity Beta-thalassemia HBB/LCRB, 8 conditions, Beta-thalassemia HBB/LCRB
RS193922561 Health Risk Conflicting classifications of pathogenicity
RS193922562 Health Risk Conflicting classifications of pathogenicity Fetal hemoglobin quantitative trait locus 1, beta Thalassemia, Hemoglobin E
RS2494295133 Health Risk Conflicting classifications of pathogenicity Malaria, susceptibility to, Malaria
RS33914359 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN N (BALTIMORE), HEMOGLOBIN N (JENKINS), HEMOGLOBIN JENKINS
RS33932070 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN G (COPENHAGEN), HEMOGLOBIN G (COPENHAGEN)
RS33935673 Health Risk Conflicting classifications of pathogenicity
RS33936254 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN G (SASKATOON), HEMOGLOBIN G (TAEGU), HEMOGLOBIN G (COUSHATTA)
RS33945705 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN KORLE-BU, beta Thalassemia, HEMOGLOBIN KORLE-BU
RS33947020 Health Risk Conflicting classifications of pathogenicity
RS33947415 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN CITY OF HOPE, beta Thalassemia, Fetal hemoglobin quantitative trait locus 1
RS33949486 Health Risk Conflicting classifications of pathogenicity beta Thalassemia, Hb SS disease, Inborn genetic diseases
RS33949930 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN RALEIGH, beta Thalassemia, HEMOGLOBIN RALEIGH
RS33957964 Health Risk Conflicting classifications of pathogenicity
RS33958088 Health Risk Conflicting classifications of pathogenicity beta Thalassemia, Fetal hemoglobin quantitative trait locus 1, Hemoglobin E
RS33958358 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN SOUTH FLORIDA, beta Thalassemia, HEMOGLOBIN SOUTH FLORIDA
RS33960931 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN COLIMA, HEMOGLOBIN COLIMA
RS33961886 Health Risk Conflicting classifications of pathogenicity beta Thalassemia, beta Thalassemia
RS33962676 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN J (BALTIMORE), HEMOGLOBIN J (BALTIMORE)
RS33966761 Health Risk Conflicting classifications of pathogenicity Hemoglobinopathy, HEMOGLOBIN YAOUNDE, beta Thalassemia
RS33982568 Health Risk Conflicting classifications of pathogenicity Beta zero thalassemia, beta Thalassemia, 8 conditions
RS33983205 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN DEER LODGE, HEMOGLOBIN DEER LODGE
RS33983276 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN KHARTOUM, Hemoglobinopathy, HEMOGLOBIN KHARTOUM
RS33987957 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN BEOGRAD, HEMOGLOBIN D (CAMPERDOWN), 8 conditions
RS33991294 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN J (IRAN), HEMOGLOBIN J (IRAN)
RS33993004 Health Risk Conflicting classifications of pathogenicity HEMOGLOBIN VILA REAL, Erythrocytosis, familial
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