GSN Chromosome 9

Gelsolin
62 variants 62 Health Risk

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What This Gene Does
The protein encoded by this gene binds to the "plus" ends of actin monomers and filaments to prevent monomer exchange. The encoded calcium-regulated protein functions in both assembly and disassembly of actin filaments. Defects in this gene are a cause of familial amyloidosis Finnish type (FAF). Multiple transcript variants encoding several different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Gelsolin/villins
Locus Type
gene with protein product
Location
9q33.2
Ensembl
ENSG00000148180
Associated Conditions (3)
Inborn genetic diseases
Finnish type amyloidosis
GSN-related disorder
Key Variants
RS1199158051
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS1275798438
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS138068754
Conflicting classifications of pathogenicity
Finnish type amyloidosis, Inborn genetic diseases, Finnish type amyloidosis
Health Risk
RS138153246
Conflicting classifications of pathogenicity
Health Risk
RS141314418
Conflicting classifications of pathogenicity
Inborn genetic diseases, Finnish type amyloidosis, Inborn genetic diseases
Health Risk
RS141510612
Conflicting classifications of pathogenicity
Finnish type amyloidosis, Inborn genetic diseases, Finnish type amyloidosis
Health Risk
RS142034230
Conflicting classifications of pathogenicity
Finnish type amyloidosis, Inborn genetic diseases, Finnish type amyloidosis
Health Risk
RS142305374
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS142828669
Conflicting classifications of pathogenicity
Finnish type amyloidosis, Inborn genetic diseases, Finnish type amyloidosis
Health Risk
RS144375242
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS145066574
Conflicting classifications of pathogenicity
Finnish type amyloidosis, Finnish type amyloidosis
Health Risk
RS145170518
Conflicting classifications of pathogenicity
Finnish type amyloidosis, Finnish type amyloidosis
Health Risk
All Variants (62)
RSID Category Clinical Significance Conditions
RS770023727 Health Risk Conflicting classifications of pathogenicity Finnish type amyloidosis, Finnish type amyloidosis
RS776618806 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS777955781 Health Risk Conflicting classifications of pathogenicity Finnish type amyloidosis, Finnish type amyloidosis
RS779179398 Health Risk Conflicting classifications of pathogenicity
RS779756580 Health Risk Conflicting classifications of pathogenicity Finnish type amyloidosis, Finnish type amyloidosis
RS780252276 Health Risk Conflicting classifications of pathogenicity
RS781764487 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Finnish type amyloidosis, Inborn genetic diseases
RS886063405 Health Risk Conflicting classifications of pathogenicity Finnish type amyloidosis, Inborn genetic diseases, Finnish type amyloidosis
RS2059635206 Health Risk Likely pathogenic Finnish type amyloidosis, Finnish type amyloidosis
RS1564564688 Health Risk Pathogenic Finnish type amyloidosis, Finnish type amyloidosis
RS2133433678 Health Risk Pathogenic Finnish type amyloidosis, Finnish type amyloidosis
RS121909715 Health Risk Pathogenic/Likely pathogenic Finnish type amyloidosis, Inborn genetic diseases, Finnish type amyloidosis
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