GPR143 Chromosome X

G protein-coupled receptor 143
99 variants 99 Health Risk

Upload your DNA to see your personal genotypes for variants in GPR143.

What This Gene Does
This gene encodes a protein that binds to heterotrimeric G proteins and is targeted to melanosomes in pigment cells. This protein is thought to be involved in intracellular signal transduction mechanisms. Mutations in this gene cause ocular albinism type 1, also referred to as Nettleship-Falls type ocular albinism, a severe visual disorder. A related pseudogene has been identified on chromosome Y. [provided by RefSeq, Dec 2009]
Gene Info
Gene Group
7TM uncharacterized proteins
Locus Type
gene with protein product
Location
Xp22.2
Ensembl
ENSG00000101850
Associated Conditions (12)
Ocular albinism
type I
Inborn genetic diseases
Nystagmus 6
congenital
X-linked
GPR143-related foveal hypoplasia
Albinism
Retinal disorder
GPR143-related disorder
Nystagmus
Reduced eye contact
Key Variants
All Variants (99)
RSID Category Clinical Significance Conditions
RS1055796261 Health Risk Conflicting classifications of pathogenicity
RS137852297 Health Risk Conflicting classifications of pathogenicity Ocular albinism, type I, Inborn genetic diseases
RS137938780 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS138809166 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS149605054 Health Risk Conflicting classifications of pathogenicity
RS200574016 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS200870584 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS201596200 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS2146700794 Health Risk Conflicting classifications of pathogenicity
RS374596288 Health Risk Conflicting classifications of pathogenicity
RS375563631 Health Risk Conflicting classifications of pathogenicity
RS62635037 Health Risk Conflicting classifications of pathogenicity
RS754693386 Health Risk Conflicting classifications of pathogenicity
RS759315924 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS776232889 Health Risk Conflicting classifications of pathogenicity Ocular albinism, type I, Ocular albinism
RS925889440 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS2083394185 Health Risk Likely pathogenic Ocular albinism, type I, Nystagmus 6
RS2146684218 Health Risk Likely pathogenic
RS2146685691 Health Risk Likely pathogenic
RS2146687459 Health Risk Likely pathogenic Ocular albinism, type I, Ocular albinism
RS2146691632 Health Risk Likely pathogenic Ocular albinism, type I, Ocular albinism
RS2146699662 Health Risk Likely pathogenic
RS2146705592 Health Risk Likely pathogenic
RS2518626868 Health Risk Likely pathogenic
RS2518637181 Health Risk Likely pathogenic
RS2518638150 Health Risk Likely pathogenic Nystagmus 6, congenital, X-linked
RS2518641943 Health Risk Likely pathogenic Ocular albinism, type I, Ocular albinism
RS281865178 Health Risk Likely pathogenic Ocular albinism, type I, Nystagmus 6
RS281865179 Health Risk Likely pathogenic
RS281865181 Health Risk Likely pathogenic
RS62635031 Health Risk Likely pathogenic
RS62635042 Health Risk Likely pathogenic Albinism, Albinism
RS62635046 Health Risk Likely pathogenic
RS672601353 Health Risk Likely pathogenic Ocular albinism, type I, Ocular albinism
RS761860018 Health Risk Likely pathogenic
RS1057518164 Health Risk Pathogenic Retinal disorder, Retinal disorder
RS1057520200 Health Risk Pathogenic
RS1191147473 Health Risk Pathogenic
RS1251267106 Health Risk Pathogenic Ocular albinism, type I, Ocular albinism
RS137852296 Health Risk Pathogenic Ocular albinism, type I, Nystagmus 6
RS137852298 Health Risk Pathogenic Nystagmus 6, congenital, X-linked
RS148358078 Health Risk Pathogenic
RS1555914303 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS1569118851 Health Risk Pathogenic Nystagmus 6, congenital, X-linked
RS1601880424 Health Risk Pathogenic
RS2083414866 Health Risk Pathogenic
RS2083438278 Health Risk Pathogenic Ocular albinism, type I, Ocular albinism
RS2083486427 Health Risk Pathogenic
RS2146684328 Health Risk Pathogenic GPR143-related disorder, GPR143-related disorder
RS2146685694 Health Risk Pathogenic
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