GJA8 Chromosome 1

Gap junction protein alpha 8
57 variants 57 Health Risk

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What This Gene Does
This gene encodes a transmembrane connexin protein that is necessary for lens growth and maturation of lens fiber cells. The encoded protein is a component of gap junction channels and functions in a calcium and pH-dependent manner. Mutations in this gene have been associated with zonular pulverulent cataracts, nuclear progressive cataracts, and cataract-microcornea syndrome. [provided by RefSeq, Dec 2009]
Gene Info
Gene Group
Gap junction proteins
Locus Type
gene with protein product
Location
1q21.2
Ensembl
ENSG00000121634
Associated Conditions (9)
Cataract 1 multiple types
GJA8-related disorder
Inborn genetic diseases
Anterior segment dysgenesis
Developmental cataract
acorea
microphthalmia and cataract syndrome
Microphthalmia
acorea-microphthalmia-cataract syndrome
Key Variants
RS150441169
Conflicting classifications of pathogenicity
Cataract 1 multiple types, GJA8-related disorder, Cataract 1 multiple types
Health Risk
RS1553242554
Conflicting classifications of pathogenicity
Inborn genetic diseases, Cataract 1 multiple types, Inborn genetic diseases
Health Risk
RS1553242577
Conflicting classifications of pathogenicity
Cataract 1 multiple types, Cataract 1 multiple types
Health Risk
RS1651887395
Conflicting classifications of pathogenicity
Anterior segment dysgenesis, Cataract 1 multiple types, Anterior segment dysgenesis
Health Risk
RS1651887603
Conflicting classifications of pathogenicity
Anterior segment dysgenesis, Cataract 1 multiple types, Anterior segment dysgenesis
Health Risk
RS1651918704
Conflicting classifications of pathogenicity
Cataract 1 multiple types, Cataract 1 multiple types
Health Risk
RS1651922680
Conflicting classifications of pathogenicity
GJA8-related disorder, GJA8-related disorder
Health Risk
RS1651940183
Conflicting classifications of pathogenicity
Cataract 1 multiple types, Cataract 1 multiple types
Health Risk
RS2149015482
Conflicting classifications of pathogenicity
Cataract 1 multiple types, Cataract 1 multiple types
Health Risk
RS2149015924
Conflicting classifications of pathogenicity
Developmental cataract, Cataract 1 multiple types, Developmental cataract
Health Risk
RS2524888276
Conflicting classifications of pathogenicity
Cataract 1 multiple types, Cataract 1 multiple types
Health Risk
RS2524889089
Conflicting classifications of pathogenicity
Cataract 1 multiple types, Cataract 1 multiple types
Health Risk
All Variants (57)
RSID Category Clinical Significance Conditions
RS150441169 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, GJA8-related disorder, Cataract 1 multiple types
RS1553242554 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Cataract 1 multiple types, Inborn genetic diseases
RS1553242577 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS1651887395 Health Risk Conflicting classifications of pathogenicity Anterior segment dysgenesis, Cataract 1 multiple types, Anterior segment dysgenesis
RS1651887603 Health Risk Conflicting classifications of pathogenicity Anterior segment dysgenesis, Cataract 1 multiple types, Anterior segment dysgenesis
RS1651918704 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS1651922680 Health Risk Conflicting classifications of pathogenicity GJA8-related disorder, GJA8-related disorder
RS1651940183 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS2149015482 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS2149015924 Health Risk Conflicting classifications of pathogenicity Developmental cataract, Cataract 1 multiple types, Developmental cataract
RS2524888276 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS2524889089 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS2524889140 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, acorea, microphthalmia and cataract syndrome
RS2524889961 Health Risk Conflicting classifications of pathogenicity GJA8-related disorder, Cataract 1 multiple types, GJA8-related disorder
RS2524889972 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS2524891845 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS2524891883 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS781881392 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, GJA8-related disorder, Inborn genetic diseases
RS781949456 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS782054970 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Cataract 1 multiple types, Inborn genetic diseases
RS782505421 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Inborn genetic diseases, Cataract 1 multiple types
RS80358200 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types, Cataract 1 multiple types
RS80358201 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS80358204 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS80358205 Health Risk Conflicting classifications of pathogenicity Cataract 1 multiple types, Cataract 1 multiple types
RS1571175899 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS2149015335 Health Risk Likely pathogenic Developmental cataract, Cataract 1 multiple types, Cataract 1 multiple types
RS2149015516 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS2524888659 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS2524888804 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS2524888892 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS2524889317 Health Risk Likely pathogenic Microphthalmia, Cataract 1 multiple types, Microphthalmia
RS2524889327 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types, Cataract 1 multiple types
RS2524889489 Health Risk Likely pathogenic
RS2524889508 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS2524889513 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS2524891019 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS2524891890 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS2524892983 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS782199122 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types, Cataract 1 multiple types
RS782285117 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS80358203 Health Risk Likely pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS864309684 Health Risk Likely pathogenic Developmental cataract, Cataract 1 multiple types, Developmental cataract
RS864309703 Health Risk Likely pathogenic Developmental cataract, Cataract 1 multiple types, acorea-microphthalmia-cataract syndrome
RS1307969607 Health Risk Pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS1571175950 Health Risk Pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS1651879427 Health Risk Pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS1651881222 Health Risk Pathogenic Cataract 1 multiple types, Cataract 1 multiple types, Cataract 1 multiple types
RS1651919374 Health Risk Pathogenic Cataract 1 multiple types, Cataract 1 multiple types
RS2149015418 Health Risk Pathogenic Cataract 1 multiple types, Cataract 1 multiple types
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