FZD4 Chromosome 11

Frizzled class receptor 4
80 variants 80 Health Risk

Upload your DNA to see your personal genotypes for variants in FZD4.

What This Gene Does
This gene is a member of the frizzled gene family. Members of this family encode seven-transmembrane domain proteins that are receptors for the Wingless type MMTV integration site family of signaling proteins. Most frizzled receptors are coupled to the beta-catenin canonical signaling pathway. This protein may play a role as a positive regulator of the Wingless type MMTV integration site signaling pathway. A transcript variant retaining intronic sequence and encoding a shorter isoform has been described, however, its expression is not supported by other experimental evidence. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
"G protein-coupled receptors, Class F frizzled|CD molecules"
Locus Type
gene with protein product
Location
11q14.2
Ensembl
ENSG00000174804
Associated Conditions (10)
Inborn genetic diseases
Retinopathy of prematurity
FZD4-related disorder
Exudative vitreoretinopathy 1
Retinal dystrophy
Familial exudative vitreoretinopathy
Coats disease
Atrophia bulborum hereditaria
Exudative vitreoretinopathy
digenic
Key Variants
All Variants (80)
RSID Category Clinical Significance Conditions
RS1036091905 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS104894223 Health Risk Conflicting classifications of pathogenicity Retinopathy of prematurity, FZD4-related disorder, Retinopathy of prematurity
RS1050752347 Health Risk Conflicting classifications of pathogenicity Exudative vitreoretinopathy 1, Exudative vitreoretinopathy 1
RS113917021 Health Risk Conflicting classifications of pathogenicity
RS1280981405 Health Risk Conflicting classifications of pathogenicity Exudative vitreoretinopathy 1, Exudative vitreoretinopathy 1
RS140601725 Health Risk Conflicting classifications of pathogenicity Exudative vitreoretinopathy 1, Exudative vitreoretinopathy 1
RS146895719 Health Risk Conflicting classifications of pathogenicity Exudative vitreoretinopathy 1, Inborn genetic diseases, Exudative vitreoretinopathy 1
RS147766472 Health Risk Conflicting classifications of pathogenicity
RS148672481 Health Risk Conflicting classifications of pathogenicity
RS1949297493 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS201256460 Health Risk Conflicting classifications of pathogenicity Exudative vitreoretinopathy 1, Exudative vitreoretinopathy 1
RS376854255 Health Risk Conflicting classifications of pathogenicity Exudative vitreoretinopathy 1, Retinal dystrophy, Exudative vitreoretinopathy 1
RS377443153 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS560649393 Health Risk Conflicting classifications of pathogenicity
RS756119359 Health Risk Conflicting classifications of pathogenicity
RS769786110 Health Risk Conflicting classifications of pathogenicity Exudative vitreoretinopathy 1, Exudative vitreoretinopathy 1
RS80358282 Health Risk Conflicting classifications of pathogenicity Exudative vitreoretinopathy 1, Retinal dystrophy, Exudative vitreoretinopathy 1
RS1064793132 Health Risk Likely pathogenic
RS1408259285 Health Risk Likely pathogenic Exudative vitreoretinopathy 1, Exudative vitreoretinopathy 1
RS1555085564 Health Risk Likely pathogenic
RS1590943821 Health Risk Likely pathogenic
RS1949299271 Health Risk Likely pathogenic Exudative vitreoretinopathy 1, Exudative vitreoretinopathy 1
RS2135040558 Health Risk Likely pathogenic
RS2135041940 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS2495865897 Health Risk Likely pathogenic
RS2495867722 Health Risk Likely pathogenic Exudative vitreoretinopathy 1, Exudative vitreoretinopathy 1
RS759432455 Health Risk Likely pathogenic Familial exudative vitreoretinopathy, Familial exudative vitreoretinopathy
RS80358285 Health Risk Likely pathogenic
RS886039372 Health Risk Likely pathogenic
RS1064794064 Health Risk Pathogenic
RS139401671 Health Risk Pathogenic
RS1555085637 Health Risk Pathogenic
RS1555086007 Health Risk Pathogenic Familial exudative vitreoretinopathy, Familial exudative vitreoretinopathy
RS1949288383 Health Risk Pathogenic
RS1949288787 Health Risk Pathogenic
RS1949298315 Health Risk Pathogenic
RS1949299681 Health Risk Pathogenic
RS1949300253 Health Risk Pathogenic
RS1949320566 Health Risk Pathogenic
RS1949323335 Health Risk Pathogenic
RS1949325180 Health Risk Pathogenic
RS2135039721 Health Risk Pathogenic
RS2135040070 Health Risk Pathogenic
RS2135040093 Health Risk Pathogenic
RS2135040135 Health Risk Pathogenic
RS2135040415 Health Risk Pathogenic
RS2135041449 Health Risk Pathogenic
RS2495864907 Health Risk Pathogenic
RS2495864953 Health Risk Pathogenic
RS2495866103 Health Risk Pathogenic Exudative vitreoretinopathy 1, Exudative vitreoretinopathy 1
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