FOXG1 Chromosome 14

Forkhead box G1
235 variants 235 Health Risk

Upload your DNA to see your personal genotypes for variants in FOXG1.

What This Gene Does
This locus encodes a member of the fork-head transcription factor family. The encoded protein, which functions as a transcriptional repressor, is highly expressed in neural tissues during brain development. Mutations at this locus have been associated with Rett syndrome and a diverse spectrum of neurodevelopmental disorders defined as part of the FOXG1 syndrome. This gene is disregulated in many types of cancer and is the target of multiple microRNAs that regulate the proliferation of tumor cells. [provided by RefSeq, Jul 2020]
Gene Info
Gene Group
Forkhead boxes
Locus Type
gene with protein product
Location
14q12
Ensembl
ENSG00000176165
Associated Conditions (18)
FOXG1 disorder
Inborn genetic diseases
Primary microcephaly
Severe intellectual disability
Aplasia/Hypoplasia of the corpus callosum
Rett syndrome
Lissencephaly
FOXG1-related disorder
Intellectual disability
Neurodevelopmental disorder
Strabismus
Abnormal optic nerve morphology
Global developmental delay
Axial hypotonia
Stereotypic movement disorder
Abnormal cerebral morphology
Abnormality of the nervous system
Severe intellectual deficiency
Key Variants
All Variants (235)
RSID Category Clinical Significance Conditions
RS786205486 Health Risk Pathogenic Rett syndrome, FOXG1 disorder, Rett syndrome
RS796052458 Health Risk Pathogenic
RS796052461 Health Risk Pathogenic Severe intellectual deficiency, FOXG1 disorder, FOXG1 disorder
RS796052462 Health Risk Pathogenic Inborn genetic diseases, FOXG1 disorder, Inborn genetic diseases
RS796052463 Health Risk Pathogenic FOXG1 disorder, FOXG1 disorder
RS796052464 Health Risk Pathogenic FOXG1 disorder, FOXG1 disorder
RS796052465 Health Risk Pathogenic
RS796052468 Health Risk Pathogenic
RS796052474 Health Risk Pathogenic FOXG1 disorder, FOXG1 disorder, FOXG1 disorder
RS796052476 Health Risk Pathogenic
RS796052477 Health Risk Pathogenic
RS796052485 Health Risk Pathogenic
RS796052486 Health Risk Pathogenic FOXG1 disorder, FOXG1 disorder
RS797045583 Health Risk Pathogenic FOXG1 disorder, FOXG1 disorder
RS869312700 Health Risk Pathogenic FOXG1 disorder, FOXG1 disorder, FOXG1 disorder
RS869312961 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS886041744 Health Risk Pathogenic FOXG1 disorder, FOXG1 disorder, FOXG1 disorder
RS1555321301 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS1555321302 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS1555321325 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, Inborn genetic diseases, FOXG1 disorder
RS1555321353 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS1566445489 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, Neurodevelopmental disorder, FOXG1 disorder
RS1881802605 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, Rett syndrome, FOXG1 disorder
RS1881804364 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS1881808715 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS2138661170 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder, Inborn genetic diseases
RS2138661213 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS2138661448 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS587783641 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS786204998 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS786205005 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, Inborn genetic diseases, FOXG1 disorder
RS786205006 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS786205008 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS786205009 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
RS786205011 Health Risk Pathogenic/Likely pathogenic FOXG1 disorder, FOXG1 disorder
« Prev 1 2 3 4 5
Sign Up to Analyze Your DNA Log In