FGF23 Chromosome 12

Fibroblast growth factor 23
25 variants 25 Health Risk

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What This Gene Does
This gene encodes a member of the fibroblast growth factor family of proteins, which possess broad mitogenic and cell survival activities and are involved in a variety of biological processes. The product of this gene regulates phosphate homeostasis and transport in the kidney. The full-length, functional protein may be deactivated via cleavage into N-terminal and C-terminal chains. Mutation of this cleavage site causes autosomal dominant hypophosphatemic rickets (ADHR). Mutations in this gene are also associated with hyperphosphatemic familial tumoral calcinosis (HFTC). [provided by RefSeq, Feb 2013]
Gene Info
Gene Group
"Receptor ligands|Fibroblast growth factor family"
Locus Type
gene with protein product
Location
12p13.32
Ensembl
ENSG00000118972
Associated Conditions (10)
Tumoral calcinosis
hyperphosphatemic
familial
1
2
Familial hyperphosphatemic tumoral calcinosis/hyperphosphatemic hyperostosis syndrome
Autosomal dominant hypophosphatemic rickets
Inborn genetic diseases
Hypophosphatemic rickets
Short stature
Key Variants
All Variants (25)
RSID Category Clinical Significance Conditions
RS104894342 Health Risk Conflicting classifications of pathogenicity Tumoral calcinosis, hyperphosphatemic, familial
RS1064795205 Health Risk Conflicting classifications of pathogenicity
RS13312800 Health Risk Conflicting classifications of pathogenicity Tumoral calcinosis, hyperphosphatemic, familial
RS13312801 Health Risk Conflicting classifications of pathogenicity Tumoral calcinosis, hyperphosphatemic, familial
RS144925325 Health Risk Conflicting classifications of pathogenicity Autosomal dominant hypophosphatemic rickets, Tumoral calcinosis, hyperphosphatemic
RS183802802 Health Risk Conflicting classifications of pathogenicity Tumoral calcinosis, hyperphosphatemic, familial
RS190841442 Health Risk Conflicting classifications of pathogenicity Tumoral calcinosis, hyperphosphatemic, familial
RS368115734 Health Risk Conflicting classifications of pathogenicity Autosomal dominant hypophosphatemic rickets, Tumoral calcinosis, hyperphosphatemic
RS531815578 Health Risk Conflicting classifications of pathogenicity Tumoral calcinosis, hyperphosphatemic, familial
RS566868058 Health Risk Conflicting classifications of pathogenicity Autosomal dominant hypophosphatemic rickets, Tumoral calcinosis, hyperphosphatemic
RS573322878 Health Risk Conflicting classifications of pathogenicity Tumoral calcinosis, hyperphosphatemic, familial
RS753676774 Health Risk Conflicting classifications of pathogenicity Autosomal dominant hypophosphatemic rickets, Tumoral calcinosis, hyperphosphatemic
RS758725402 Health Risk Conflicting classifications of pathogenicity Tumoral calcinosis, hyperphosphatemic, familial
RS765478662 Health Risk Conflicting classifications of pathogenicity Autosomal dominant hypophosphatemic rickets, Tumoral calcinosis, hyperphosphatemic
RS193922701 Health Risk Likely pathogenic Autosomal dominant hypophosphatemic rickets, Autosomal dominant hypophosphatemic rickets
RS2497236074 Health Risk Likely pathogenic Autosomal dominant hypophosphatemic rickets, Autosomal dominant hypophosphatemic rickets
RS863224872 Health Risk Likely pathogenic Familial hyperphosphatemic tumoral calcinosis/hyperphosphatemic hyperostosis syndrome, Familial hyperphosphatemic tumoral calcinosis/hyperphosphatemic hyperostosis syndrome
RS104894343 Health Risk Pathogenic Tumoral calcinosis, hyperphosphatemic, familial
RS104894344 Health Risk Pathogenic Tumoral calcinosis, hyperphosphatemic, familial
RS104894347 Health Risk Pathogenic Autosomal dominant hypophosphatemic rickets, Autosomal dominant hypophosphatemic rickets
RS193922702 Health Risk Pathogenic Autosomal dominant hypophosphatemic rickets, Hypophosphatemic rickets, Tumoral calcinosis
RS754201217 Health Risk Pathogenic
RS1220533001 Health Risk Pathogenic/Likely pathogenic Tumoral calcinosis, hyperphosphatemic, familial
RS1555096583 Health Risk Pathogenic/Likely pathogenic Tumoral calcinosis, hyperphosphatemic, familial
RS28937882 Health Risk Pathogenic/Likely pathogenic Autosomal dominant hypophosphatemic rickets, Autosomal dominant hypophosphatemic rickets
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