EVC Chromosome 4

EvC ciliary complex subunit 1
342 variants 342 Health Risk

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What This Gene Does
This gene encodes a protein containing a leucine zipper and a transmembrane domain. This gene has been implicated in both Ellis-van Creveld syndrome (EvC) and Weyers acrodental dysostosis. [provided by RefSeq, Jul 2008]
Associated Conditions (11)
Ellis-van Creveld syndrome
Curry-Hall syndrome
Inborn genetic diseases
EVC-related disorder
Malignant tumor of esophagus
Uterine corpus endometrial carcinoma
Clear cell carcinoma of kidney
Short-rib thoracic dysplasia 6 with or without polydactyly
Hepatocellular carcinoma
EVC-associated disorder
Chronic lymphocytic leukemia/small lymphocytic lymphoma
Key Variants
RS1035520087
Conflicting classifications of pathogenicity
Ellis-van Creveld syndrome, Curry-Hall syndrome, Inborn genetic diseases
Health Risk
RS113002470
Conflicting classifications of pathogenicity
Ellis-van Creveld syndrome, Curry-Hall syndrome, Inborn genetic diseases
Health Risk
RS115507440
Conflicting classifications of pathogenicity
Ellis-van Creveld syndrome, Curry-Hall syndrome, Inborn genetic diseases
Health Risk
RS1219807707
Conflicting classifications of pathogenicity
Ellis-van Creveld syndrome, Curry-Hall syndrome, EVC-related disorder
Health Risk
RS1237999856
Conflicting classifications of pathogenicity
Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
Health Risk
RS1252318929
Conflicting classifications of pathogenicity
Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
Health Risk
RS1314509668
Conflicting classifications of pathogenicity
Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
Health Risk
RS1361442490
Conflicting classifications of pathogenicity
Ellis-van Creveld syndrome, Curry-Hall syndrome, Inborn genetic diseases
Health Risk
RS1373148885
Conflicting classifications of pathogenicity
Ellis-van Creveld syndrome, Curry-Hall syndrome, Inborn genetic diseases
Health Risk
RS1373632260
Conflicting classifications of pathogenicity
Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
Health Risk
RS138808610
Conflicting classifications of pathogenicity
Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
Health Risk
RS139157869
Conflicting classifications of pathogenicity
Ellis-van Creveld syndrome, Curry-Hall syndrome, Inborn genetic diseases
Health Risk
All Variants (342)
RSID Category Clinical Significance Conditions
RS2152326544 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2152326770 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2152340509 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2152345583 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2152375194 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2152375437 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Hepatocellular carcinoma
RS2152387847 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2152391901 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2474190601 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474193970 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2474198889 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2474373415 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474373707 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474375517 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474384588 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474386484 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474424005 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474506697 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474507123 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2474507433 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474564704 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474566006 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2474608949 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2474611174 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2474656314 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474672497 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474673222 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474716743 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2474944725 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2475060255 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS2475159965 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2475161097 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2475165782 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2475379255 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2475379592 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2475384000 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2475385732 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, EVC-related disorder
RS2475425024 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS2476467657 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS373088008 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS374752679 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS527255616 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS539010490 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS553634958 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS587776619 Health Risk Pathogenic Ellis-van Creveld syndrome, Ellis-van Creveld syndrome
RS745627738 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS748201094 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
RS748523193 Health Risk Pathogenic Short-rib thoracic dysplasia 6 with or without polydactyly, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS751772225 Health Risk Pathogenic Curry-Hall syndrome, Ellis-van Creveld syndrome, Curry-Hall syndrome
RS753014919 Health Risk Pathogenic Ellis-van Creveld syndrome, Curry-Hall syndrome, Ellis-van Creveld syndrome
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