EMC1 Chromosome 1

ER membrane protein complex subunit 1
95 variants 95 Health Risk

Upload your DNA to see your personal genotypes for variants in EMC1.

What This Gene Does
This gene encodes a single-pass type I transmembrane protein, which is a subunit of the endoplasmic reticulum membrane protein complex (EMC). Multiple alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Sep 2012]
Gene Info
Gene Group
ER membrane protein complex subunits
Locus Type
gene with protein product
Location
1p36.13
Ensembl
ENSG00000127463
Associated Conditions (13)
Global developmental delay
Cerebellar atrophy
Inborn genetic diseases
Retinal dystrophy
visual impairment
and psychomotor retardation
Ovarian serous cystadenocarcinoma
Lung cancer
Retinitis pigmentosa
EMC1-related disorder
Autosomal recessive retinitis pigmentosa
Obesity
Congenital anomaly of kidney and urinary tract
Key Variants
RS1267383375
Conflicting classifications of pathogenicity
Global developmental delay, Cerebellar atrophy, Global developmental delay
Health Risk
RS1323481821
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS1439129239
Conflicting classifications of pathogenicity
Retinal dystrophy, Retinal dystrophy
Health Risk
RS144675935
Conflicting classifications of pathogenicity
Cerebellar atrophy, visual impairment, and psychomotor retardation
Health Risk
RS145741156
Conflicting classifications of pathogenicity
Health Risk
RS148338469
Conflicting classifications of pathogenicity
Cerebellar atrophy, visual impairment, and psychomotor retardation
Health Risk
RS149268308
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS1553252938
Conflicting classifications of pathogenicity
Inborn genetic diseases, Cerebellar atrophy, visual impairment
Health Risk
RS201537299
Conflicting classifications of pathogenicity
Inborn genetic diseases, Retinal dystrophy, Inborn genetic diseases
Health Risk
RS2093442517
Conflicting classifications of pathogenicity
Inborn genetic diseases, Cerebellar atrophy, visual impairment
Health Risk
RS2275402
Conflicting classifications of pathogenicity
Retinal dystrophy, Inborn genetic diseases, Cerebellar atrophy
Health Risk
RS537594873
Conflicting classifications of pathogenicity
Inborn genetic diseases, Retinitis pigmentosa, Inborn genetic diseases
Health Risk
All Variants (95)
RSID Category Clinical Significance Conditions
RS1267383375 Health Risk Conflicting classifications of pathogenicity Global developmental delay, Cerebellar atrophy, Global developmental delay
RS1323481821 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1439129239 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS144675935 Health Risk Conflicting classifications of pathogenicity Cerebellar atrophy, visual impairment, and psychomotor retardation
RS145741156 Health Risk Conflicting classifications of pathogenicity
RS148338469 Health Risk Conflicting classifications of pathogenicity Cerebellar atrophy, visual impairment, and psychomotor retardation
RS149268308 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1553252938 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Cerebellar atrophy, visual impairment
RS201537299 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Retinal dystrophy, Inborn genetic diseases
RS2093442517 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Cerebellar atrophy, visual impairment
RS2275402 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Inborn genetic diseases, Cerebellar atrophy
RS537594873 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Retinitis pigmentosa, Inborn genetic diseases
RS561638764 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS746674701 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS752777483 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, EMC1-related disorder, Retinal dystrophy
RS758051221 Health Risk Conflicting classifications of pathogenicity Cerebellar atrophy, visual impairment, and psychomotor retardation
RS760060777 Health Risk Conflicting classifications of pathogenicity Cerebellar atrophy, visual impairment, and psychomotor retardation
RS764914973 Health Risk Conflicting classifications of pathogenicity
RS766820627 Health Risk Conflicting classifications of pathogenicity Cerebellar atrophy, visual impairment, and psychomotor retardation
RS778418940 Health Risk Conflicting classifications of pathogenicity
RS781137936 Health Risk Conflicting classifications of pathogenicity Cerebellar atrophy, visual impairment, and psychomotor retardation
RS869320623 Health Risk Conflicting classifications of pathogenicity Autosomal recessive retinitis pigmentosa, Cerebellar atrophy, visual impairment
RS1258131141 Health Risk Likely pathogenic Cerebellar atrophy, visual impairment, and psychomotor retardation
RS1261194928 Health Risk Likely pathogenic
RS1431810286 Health Risk Likely pathogenic
RS145763979 Health Risk Likely pathogenic
RS150431800 Health Risk Likely pathogenic
RS1571963780 Health Risk Likely pathogenic
RS1572001567 Health Risk Likely pathogenic Cerebellar atrophy, visual impairment, and psychomotor retardation
RS2093588528 Health Risk Likely pathogenic
RS2093611226 Health Risk Likely pathogenic
RS2093658825 Health Risk Likely pathogenic
RS2151947969 Health Risk Likely pathogenic
RS2151949366 Health Risk Likely pathogenic
RS2151952121 Health Risk Likely pathogenic
RS2151962465 Health Risk Likely pathogenic
RS2536637199 Health Risk Likely pathogenic Cerebellar atrophy, visual impairment, and psychomotor retardation
RS2536664620 Health Risk Likely pathogenic
RS2536666629 Health Risk Likely pathogenic
RS2536760867 Health Risk Likely pathogenic
RS2536775591 Health Risk Likely pathogenic Cerebellar atrophy, visual impairment, and psychomotor retardation
RS374972410 Health Risk Likely pathogenic
RS750255505 Health Risk Likely pathogenic
RS751484278 Health Risk Likely pathogenic Cerebellar atrophy, visual impairment, and psychomotor retardation
RS772560574 Health Risk Likely pathogenic Cerebellar atrophy, visual impairment, and psychomotor retardation
RS941175056 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS951989321 Health Risk Likely pathogenic
RS998362250 Health Risk Likely pathogenic
RS1167848259 Health Risk Pathogenic
RS1193333328 Health Risk Pathogenic
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