DZIP1 Chromosome 13

DAZ interacting zinc finger protein 1
2 variants 2 Health Risk

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What This Gene Does
Enables BBSome binding activity and molecular adaptor activity. Involved in cilium organization; heart development; and protein-containing complex localization to centriolar satellite. Located in cytosol; microtubule organizing center; and nucleoplasm. Implicated in mitral valve prolapse and spermatogenic failure 47. [provided by Alliance of Genome Resources, Jul 2025]
Gene Info
Gene Group
Zinc fingers C2H2-type
Locus Type
gene with protein product
Location
13q32.1
Ensembl
ENSG00000134874
Associated Conditions (1)
Spermatogenic failure 47
Key Variants
All Variants (2)
RSID Category Clinical Significance Conditions
RS1877018344 Health Risk Pathogenic Spermatogenic failure 47, Spermatogenic failure 47
RS1878524886 Health Risk Pathogenic Spermatogenic failure 47, Spermatogenic failure 47
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