DOK7 Chromosome 4

Docking protein 7
178 variants 178 Health Risk

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What This Gene Does
The protein encoded by this gene is essential for neuromuscular synaptogenesis. The protein functions in aneural activation of muscle-specific receptor kinase, which is required for postsynaptic differentiation, and in the subsequent clustering of the acetylcholine receptor in myotubes. This protein can also induce autophosphorylation of muscle-specific receptor kinase. Mutations in this gene are a cause of familial limb-girdle myasthenia autosomal recessive, which is also known as congenital myasthenic syndrome type 1B. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Sep 2009]
Associated Conditions (10)
Congenital myasthenic syndrome 10
Fetal akinesia deformation sequence 1
Inborn genetic diseases
DOK7-related disorder
Fetal akinesia deformation sequence 3
Congenital myasthenic syndrome
See cases
Ritscher-Schinzel syndrome 2
Rett syndrome
Abnormality of the musculature
Key Variants
RS115614731
Conflicting classifications of pathogenicity
Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1, Inborn genetic diseases
Health Risk
RS115883468
Conflicting classifications of pathogenicity
Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Inborn genetic diseases
Health Risk
RS1166517627
Conflicting classifications of pathogenicity
Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Inborn genetic diseases
Health Risk
RS138010842
Conflicting classifications of pathogenicity
Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
Health Risk
RS139468087
Conflicting classifications of pathogenicity
Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
Health Risk
RS141141719
Conflicting classifications of pathogenicity
Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1, DOK7-related disorder
Health Risk
RS1417673287
Conflicting classifications of pathogenicity
Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
Health Risk
RS141947707
Conflicting classifications of pathogenicity
Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
Health Risk
RS142821143
Conflicting classifications of pathogenicity
Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
Health Risk
RS144158112
Conflicting classifications of pathogenicity
Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Inborn genetic diseases
Health Risk
RS144269117
Conflicting classifications of pathogenicity
Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Inborn genetic diseases
Health Risk
RS144592743
Conflicting classifications of pathogenicity
Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, DOK7-related disorder
Health Risk
All Variants (178)
RSID Category Clinical Significance Conditions
RS762148551 Health Risk Conflicting classifications of pathogenicity Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
RS762952740 Health Risk Conflicting classifications of pathogenicity Congenital myasthenic syndrome 10, Congenital myasthenic syndrome 10
RS763494431 Health Risk Conflicting classifications of pathogenicity Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 3
RS768322699 Health Risk Conflicting classifications of pathogenicity Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
RS770163440 Health Risk Conflicting classifications of pathogenicity Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1, Fetal akinesia deformation sequence 3
RS772918388 Health Risk Conflicting classifications of pathogenicity Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10
RS773220689 Health Risk Conflicting classifications of pathogenicity Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
RS773592493 Health Risk Conflicting classifications of pathogenicity Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
RS777573281 Health Risk Conflicting classifications of pathogenicity Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, DOK7-related disorder
RS79063654 Health Risk Conflicting classifications of pathogenicity Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, DOK7-related disorder
RS940346413 Health Risk Conflicting classifications of pathogenicity Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1, DOK7-related disorder
RS118203994 Health Risk Likely pathogenic Congenital myasthenic syndrome 10, Congenital myasthenic syndrome, Congenital myasthenic syndrome 10
RS1246160310 Health Risk Likely pathogenic Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10
RS1268475752 Health Risk Likely pathogenic Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Congenital myasthenic syndrome 10
RS1286718786 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS1291304798 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS1359635065 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS1422350586 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS1449351306 Health Risk Likely pathogenic Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 3, Congenital myasthenic syndrome 10
RS1460112018 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 3
RS1480670755 Health Risk Likely pathogenic Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10
RS1490214819 Health Risk Likely pathogenic Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10
RS150376433 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS1577153029 Health Risk Likely pathogenic Congenital myasthenic syndrome 10, Congenital myasthenic syndrome 10
RS1727094027 Health Risk Likely pathogenic Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
RS1727731607 Health Risk Likely pathogenic Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10
RS1728633687 Health Risk Likely pathogenic Congenital myasthenic syndrome 10, Congenital myasthenic syndrome 10
RS2109312461 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2109369117 Health Risk Likely pathogenic Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1
RS2109388978 Health Risk Likely pathogenic Congenital myasthenic syndrome 10, Congenital myasthenic syndrome 10
RS2474962475 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475008261 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475052908 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475053000 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475076757 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475109793 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475110217 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475110434 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475110558 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475110727 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475111580 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475115215 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475115360 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475116151 Health Risk Likely pathogenic DOK7-related disorder, DOK7-related disorder
RS2475116486 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475116680 Health Risk Likely pathogenic Congenital myasthenic syndrome, Congenital myasthenic syndrome
RS2475117449 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS2475118166 Health Risk Likely pathogenic Fetal akinesia deformation sequence 3, Fetal akinesia deformation sequence 3
RS544278158 Health Risk Likely pathogenic Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10
RS571769859 Health Risk Likely pathogenic Fetal akinesia deformation sequence 1, Congenital myasthenic syndrome 10, Fetal akinesia deformation sequence 3
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