DOCK2 Chromosome 5

Dedicator of cytokinesis 2
42 variants 42 Health Risk

Upload your DNA to see your personal genotypes for variants in DOCK2.

What This Gene Does
The protein encoded by this gene belongs to the CDM protein family. It is specifically expressed in hematopoietic cells and is predominantly expressed in peripheral blood leukocytes. The protein is involved in remodeling of the actin cytoskeleton required for lymphocyte migration in response to chemokine signaling. It activates members of the Rho family of GTPases, for example RAC1 and RAC2, by acting as a guanine nucleotide exchange factor (GEF) to exchange bound GDP for free GTP. Mutations in this gene result in immunodeficiency 40 (IMD40), a combined form of immunodeficiency that affects T cell number and function, also with variable defects in B cell and NK cell function. [provided by RefSeq, May 2018]
Gene Info
Gene Group
"Armadillo like helical domain containing|DOCK family Rho GEFs|MicroRNA protein coding host genes"
Locus Type
gene with protein product
Location
5q35.1
Ensembl
ENSG00000134516
Associated Conditions (6)
DOCK2 deficiency
Pancreatic adenocarcinoma
DOCK2-related disorder
Inborn genetic diseases
See cases
Acute myeloid leukemia
Key Variants
All Variants (42)
RSID Category Clinical Significance Conditions
RS112062072 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, Pancreatic adenocarcinoma, DOCK2 deficiency
RS113289730 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2 deficiency
RS113673055 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2-related disorder, DOCK2 deficiency
RS114888195 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2-related disorder, Inborn genetic diseases
RS1295678117 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2 deficiency
RS141501849 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2-related disorder, Inborn genetic diseases
RS141894939 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2-related disorder, Inborn genetic diseases
RS143100569 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2-related disorder, Inborn genetic diseases
RS146886839 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2-related disorder, Inborn genetic diseases
RS148694888 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2 deficiency
RS149411090 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2 deficiency
RS1764493514 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, Inborn genetic diseases, DOCK2 deficiency
RS201439364 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, Inborn genetic diseases, DOCK2 deficiency
RS749326729 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, See cases, DOCK2 deficiency
RS778542070 Health Risk Conflicting classifications of pathogenicity DOCK2 deficiency, DOCK2 deficiency
RS1035797449 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS1429834722 Health Risk Likely pathogenic DOCK2 deficiency, Acute myeloid leukemia, DOCK2 deficiency
RS1561585424 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS1561898523 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS1581049599 Health Risk Likely pathogenic
RS1581531492 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS1757824003 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS1761749097 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2532467695 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2532490041 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2532522791 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2532560930 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS780318765 Health Risk Likely pathogenic DOCK2 deficiency, DOCK2 deficiency
RS142830212 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS1581090174 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS1756328793 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS1761023588 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2113279864 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2113291833 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2113355272 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2113559002 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2113843664 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2113874830 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS2532625303 Health Risk Pathogenic
RS2532626798 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS755691445 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
RS762909359 Health Risk Pathogenic DOCK2 deficiency, DOCK2 deficiency
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