DLL3 Chromosome 19

Delta like canonical Notch ligand 3
64 variants 64 Health Risk

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What This Gene Does
This gene encodes a member of the delta protein ligand family. This family functions as Notch ligands that are characterized by a DSL domain, EGF repeats, and a transmembrane domain. Mutations in this gene cause autosomal recessive spondylocostal dysostosis 1. Two transcript variants encoding distinct isoforms have been identified for this gene. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Canonical Notch ligands
Locus Type
gene with protein product
Location
19q13.2
Ensembl
ENSG00000090932
Associated Conditions (7)
Syndactyly
Spondylocostal dysostosis 1
autosomal recessive
Inborn genetic diseases
DLL3-related disorder
Hemivertebrae
Rib fusion
Key Variants
RS1013696397
Conflicting classifications of pathogenicity
Health Risk
RS138378695
Conflicting classifications of pathogenicity
Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
Health Risk
RS139297205
Conflicting classifications of pathogenicity
Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
Health Risk
RS139638161
Conflicting classifications of pathogenicity
Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
Health Risk
RS145191532
Conflicting classifications of pathogenicity
Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
Health Risk
RS147582946
Conflicting classifications of pathogenicity
Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
Health Risk
RS150100958
Conflicting classifications of pathogenicity
Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
Health Risk
RS200988915
Conflicting classifications of pathogenicity
Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
Health Risk
RS201902809
Conflicting classifications of pathogenicity
Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
Health Risk
RS2079653502
Conflicting classifications of pathogenicity
Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
Health Risk
RS372702131
Conflicting classifications of pathogenicity
Spondylocostal dysostosis 1, autosomal recessive, Spondylocostal dysostosis 1
Health Risk
RS373253569
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
All Variants (64)
RSID Category Clinical Significance Conditions
RS1013696397 Health Risk Conflicting classifications of pathogenicity
RS138378695 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS139297205 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS139638161 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS145191532 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS147582946 Health Risk Conflicting classifications of pathogenicity Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
RS150100958 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS200988915 Health Risk Conflicting classifications of pathogenicity Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
RS201902809 Health Risk Conflicting classifications of pathogenicity Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
RS2079653502 Health Risk Conflicting classifications of pathogenicity Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
RS372702131 Health Risk Conflicting classifications of pathogenicity Spondylocostal dysostosis 1, autosomal recessive, Spondylocostal dysostosis 1
RS373253569 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS373980582 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS376905666 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS528327447 Health Risk Conflicting classifications of pathogenicity Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
RS749513254 Health Risk Conflicting classifications of pathogenicity Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
RS750457185 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS759560622 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS760420806 Health Risk Conflicting classifications of pathogenicity Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
RS761480287 Health Risk Conflicting classifications of pathogenicity
RS767676342 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS777253263 Health Risk Conflicting classifications of pathogenicity Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
RS780088167 Health Risk Conflicting classifications of pathogenicity Syndactyly, Spondylocostal dysostosis 1, autosomal recessive
RS934368057 Health Risk Conflicting classifications of pathogenicity Spondylocostal dysostosis 1, autosomal recessive, Syndactyly
RS1261285510 Health Risk Likely pathogenic Spondylocostal dysostosis 1, autosomal recessive, Spondylocostal dysostosis 1
RS1447189148 Health Risk Likely pathogenic Spondylocostal dysostosis 1, autosomal recessive, Spondylocostal dysostosis 1
RS2514643690 Health Risk Likely pathogenic Spondylocostal dysostosis 1, autosomal recessive, Spondylocostal dysostosis 1
RS754886562 Health Risk Likely pathogenic
RS888371213 Health Risk Likely pathogenic Spondylocostal dysostosis 1, autosomal recessive, Spondylocostal dysostosis 1
RS962071242 Health Risk Likely pathogenic Spondylocostal dysostosis 1, autosomal recessive, Spondylocostal dysostosis 1
RS104894675 Health Risk Pathogenic Spondylocostal dysostosis 1, autosomal recessive, Spondylocostal dysostosis 1
RS1208569498 Health Risk Pathogenic
RS1243748540 Health Risk Pathogenic
RS1264168702 Health Risk Pathogenic
RS1271691132 Health Risk Pathogenic
RS1293908408 Health Risk Pathogenic
RS200275281 Health Risk Pathogenic Hemivertebrae, Rib fusion, Hemivertebrae
RS2079597067 Health Risk Pathogenic
RS2079619560 Health Risk Pathogenic
RS2079646844 Health Risk Pathogenic
RS2144761828 Health Risk Pathogenic Spondylocostal dysostosis 1, autosomal recessive, Spondylocostal dysostosis 1
RS2514640200 Health Risk Pathogenic
RS2514643983 Health Risk Pathogenic
RS2514644127 Health Risk Pathogenic
RS2514646442 Health Risk Pathogenic
RS2514646860 Health Risk Pathogenic
RS2514649158 Health Risk Pathogenic Spondylocostal dysostosis 1, autosomal recessive, Spondylocostal dysostosis 1
RS2514649349 Health Risk Pathogenic
RS2514649574 Health Risk Pathogenic
RS35667374 Health Risk Pathogenic
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