DLG4 Chromosome 17

Discs large MAGUK scaffold protein 4
87 variants 87 Health Risk

Upload your DNA to see your personal genotypes for variants in DLG4.

What This Gene Does
This gene encodes a member of the membrane-associated guanylate kinase (MAGUK) family. It heteromultimerizes with another MAGUK protein, DLG2, and is recruited into NMDA receptor and potassium channel clusters. These two MAGUK proteins may interact at postsynaptic sites to form a multimeric scaffold for the clustering of receptors, ion channels, and associated signaling proteins. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
"Membrane associated guanylate kinases|PDZ domain containing"
Locus Type
gene with protein product
Location
17p13.1
Ensembl
ENSG00000132535
Associated Conditions (7)
Inborn genetic diseases
Intellectual developmental disorder 62
Marfanoid habitus and intellectual disability
Neurodevelopmental delay
Intellectual disability
DLG4-related disorder
Cerebral visual impairment and intellectual disability
Key Variants
RS1355166210
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS2142830394
Conflicting classifications of pathogenicity
Intellectual developmental disorder 62, Intellectual developmental disorder 62
Health Risk
RS2507921984
Conflicting classifications of pathogenicity
Intellectual developmental disorder 62, Intellectual developmental disorder 62
Health Risk
RS769940216
Conflicting classifications of pathogenicity
Intellectual developmental disorder 62, Intellectual developmental disorder 62
Health Risk
RS1597444614
Likely pathogenic
Marfanoid habitus and intellectual disability, Intellectual developmental disorder 62, Marfanoid habitus and intellectual disability
Health Risk
RS2070315709
Likely pathogenic
Intellectual developmental disorder 62, Intellectual developmental disorder 62
Health Risk
RS2142825745
Likely pathogenic
Intellectual developmental disorder 62, Intellectual developmental disorder 62
Health Risk
RS2142828286
Likely pathogenic
Intellectual developmental disorder 62, Intellectual developmental disorder 62
Health Risk
RS2507910150
Likely pathogenic
Intellectual developmental disorder 62, Intellectual developmental disorder 62
Health Risk
RS2507922013
Likely pathogenic
Intellectual developmental disorder 62, Intellectual developmental disorder 62
Health Risk
RS2507926253
Likely pathogenic
Intellectual developmental disorder 62, Intellectual developmental disorder 62
Health Risk
RS2507942569
Likely pathogenic
Intellectual developmental disorder 62, Intellectual developmental disorder 62
Health Risk
All Variants (87)
RSID Category Clinical Significance Conditions
RS1355166210 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS2142830394 Health Risk Conflicting classifications of pathogenicity Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2507921984 Health Risk Conflicting classifications of pathogenicity Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS769940216 Health Risk Conflicting classifications of pathogenicity Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS1597444614 Health Risk Likely pathogenic Marfanoid habitus and intellectual disability, Intellectual developmental disorder 62, Marfanoid habitus and intellectual disability
RS2070315709 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142825745 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142828286 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2507910150 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2507922013 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2507926253 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2507942569 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2508013671 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2508015311 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2508020967 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2508023271 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2508034309 Health Risk Likely pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS1064795686 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS1160688414 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS1555522077 Health Risk Pathogenic
RS1567532079 Health Risk Pathogenic
RS1567542535 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS1597451690 Health Risk Pathogenic
RS1597452702 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS1597471063 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS1597472411 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2069778929 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2069779430 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2069827755 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2070316114 Health Risk Pathogenic
RS2142803273 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142808860 Health Risk Pathogenic
RS2142821587 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142821925 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142822298 Health Risk Pathogenic Neurodevelopmental delay, Intellectual developmental disorder 62, Neurodevelopmental delay
RS2142825224 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142828170 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142830670 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142830996 Health Risk Pathogenic Intellectual disability, Neurodevelopmental delay, Intellectual disability
RS2142843440 Health Risk Pathogenic
RS2142845390 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142885279 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142885581 Health Risk Pathogenic
RS2142885592 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142885916 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142886433 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142886600 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142886687 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
RS2142888007 Health Risk Pathogenic Intellectual developmental disorder 62, Inborn genetic diseases, Intellectual developmental disorder 62
RS2507900203 Health Risk Pathogenic Intellectual developmental disorder 62, Intellectual developmental disorder 62
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