CYP1B1 Chromosome 2

Cytochrome P450 family 1 subfamily B member 1
120 variants 120 Health Risk

Upload your DNA to see your personal genotypes for variants in CYP1B1.

What This Gene Does
This gene encodes a member of the cytochrome P450 superfamily of enzymes. The cytochrome P450 proteins are monooxygenases which catalyze many reactions involved in drug metabolism and synthesis of cholesterol, steroids and other lipids. The enzyme encoded by this gene localizes to the endoplasmic reticulum and metabolizes procarcinogens such as polycyclic aromatic hydrocarbons and 17beta-estradiol. Mutations in this gene have been associated with primary congenital glaucoma; therefore it is thought that the enzyme also metabolizes a signaling molecule involved in eye development, possibly a steroid. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Cytochrome P450 family 1
Locus Type
gene with protein product
Location
2p22.2
Ensembl
ENSG00000138061
Associated Conditions (20)
Glaucoma 3A
Primary congenital glaucoma
Congenital glaucoma
Anterior segment dysgenesis 6
Irido-corneo-trabecular dysgenesis
Ovarian serous cystadenocarcinoma
CYP1B1-related disorder
Inborn genetic diseases
Glaucoma 3
primary infantile
B
Sarcoma
CYP1B1-related glaucoma with or without anterior segment dysgenesis
Glaucoma
primary open angle
juvenile-onset
Anterior segment dysgenesis
Cataract 17 multiple types
Glaucoma of childhood
Congenital ocular coloboma
Key Variants
RS104893628
Conflicting classifications of pathogenicity
Glaucoma 3A, Primary congenital glaucoma, Congenital glaucoma
Health Risk
RS141245683
Conflicting classifications of pathogenicity
Congenital glaucoma, Glaucoma 3A, Irido-corneo-trabecular dysgenesis
Health Risk
RS1450783755
Conflicting classifications of pathogenicity
Congenital glaucoma, Glaucoma 3A, Congenital glaucoma
Health Risk
RS145847992
Conflicting classifications of pathogenicity
Congenital glaucoma, Ovarian serous cystadenocarcinoma, Congenital glaucoma
Health Risk
RS146770394
Conflicting classifications of pathogenicity
Congenital glaucoma, Irido-corneo-trabecular dysgenesis, Glaucoma 3A
Health Risk
RS148461905
Conflicting classifications of pathogenicity
Glaucoma 3A, Irido-corneo-trabecular dysgenesis, Congenital glaucoma
Health Risk
RS1682416281
Conflicting classifications of pathogenicity
Congenital glaucoma, Congenital glaucoma
Health Risk
RS1682512619
Conflicting classifications of pathogenicity
Anterior segment dysgenesis 6, Glaucoma 3A, Anterior segment dysgenesis 6
Health Risk
RS201544164
Conflicting classifications of pathogenicity
Glaucoma 3A, Glaucoma 3, primary infantile
Health Risk
RS2465878993
Conflicting classifications of pathogenicity
Anterior segment dysgenesis 6, Glaucoma 3A, Anterior segment dysgenesis 6
Health Risk
RS372321135
Conflicting classifications of pathogenicity
Congenital glaucoma, Inborn genetic diseases, Congenital glaucoma
Health Risk
RS375391843
Conflicting classifications of pathogenicity
Irido-corneo-trabecular dysgenesis, Glaucoma 3A, Congenital glaucoma
Health Risk
All Variants (120)
RSID Category Clinical Significance Conditions
RS104893628 Health Risk Conflicting classifications of pathogenicity Glaucoma 3A, Primary congenital glaucoma, Congenital glaucoma
RS141245683 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Glaucoma 3A, Irido-corneo-trabecular dysgenesis
RS1450783755 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Glaucoma 3A, Congenital glaucoma
RS145847992 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Ovarian serous cystadenocarcinoma, Congenital glaucoma
RS146770394 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Irido-corneo-trabecular dysgenesis, Glaucoma 3A
RS148461905 Health Risk Conflicting classifications of pathogenicity Glaucoma 3A, Irido-corneo-trabecular dysgenesis, Congenital glaucoma
RS1682416281 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Congenital glaucoma
RS1682512619 Health Risk Conflicting classifications of pathogenicity Anterior segment dysgenesis 6, Glaucoma 3A, Anterior segment dysgenesis 6
RS201544164 Health Risk Conflicting classifications of pathogenicity Glaucoma 3A, Glaucoma 3, primary infantile
RS2465878993 Health Risk Conflicting classifications of pathogenicity Anterior segment dysgenesis 6, Glaucoma 3A, Anterior segment dysgenesis 6
RS372321135 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Inborn genetic diseases, Congenital glaucoma
RS375391843 Health Risk Conflicting classifications of pathogenicity Irido-corneo-trabecular dysgenesis, Glaucoma 3A, Congenital glaucoma
RS4987137 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Glaucoma 3A, Irido-corneo-trabecular dysgenesis
RS56339482 Health Risk Conflicting classifications of pathogenicity Glaucoma 3A, Irido-corneo-trabecular dysgenesis, Congenital glaucoma
RS59472972 Health Risk Conflicting classifications of pathogenicity Irido-corneo-trabecular dysgenesis, Glaucoma 3A, Glaucoma 3
RS66583685 Health Risk Conflicting classifications of pathogenicity Glaucoma 3A, Glaucoma 3, primary infantile
RS72549382 Health Risk Conflicting classifications of pathogenicity Glaucoma 3A, Congenital glaucoma, Glaucoma 3
RS72549383 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Irido-corneo-trabecular dysgenesis, Glaucoma 3A
RS748708268 Health Risk Conflicting classifications of pathogenicity Glaucoma 3A, Irido-corneo-trabecular dysgenesis, Congenital glaucoma
RS749463699 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Congenital glaucoma
RS750220338 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Congenital glaucoma
RS775055418 Health Risk Conflicting classifications of pathogenicity Irido-corneo-trabecular dysgenesis, Glaucoma 3A, Congenital glaucoma
RS775908245 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Irido-corneo-trabecular dysgenesis, Glaucoma 3A
RS780375338 Health Risk Conflicting classifications of pathogenicity Irido-corneo-trabecular dysgenesis, Glaucoma 3A, Congenital glaucoma
RS9341246 Health Risk Conflicting classifications of pathogenicity Congenital glaucoma, Congenital glaucoma
RS104893622 Health Risk Likely pathogenic Glaucoma 3A, CYP1B1-related glaucoma with or without anterior segment dysgenesis, Glaucoma 3A
RS104893623 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
RS104893629 Health Risk Likely pathogenic Glaucoma, primary open angle, juvenile-onset
RS104894979 Health Risk Likely pathogenic Glaucoma 3A, Anterior segment dysgenesis 6, CYP1B1-related glaucoma with or without anterior segment dysgenesis
RS1195158694 Health Risk Likely pathogenic Anterior segment dysgenesis 6, CYP1B1-related glaucoma with or without anterior segment dysgenesis, Anterior segment dysgenesis 6
RS1267757855 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
RS1275572421 Health Risk Likely pathogenic Congenital glaucoma, Congenital glaucoma
RS147535955 Health Risk Likely pathogenic Primary congenital glaucoma, Primary congenital glaucoma
RS1558603396 Health Risk Likely pathogenic Glaucoma 3A, Anterior segment dysgenesis 6, Congenital glaucoma
RS1573274915 Health Risk Likely pathogenic Glaucoma 3A, Glaucoma 3A
RS1573276416 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
RS2125314878 Health Risk Likely pathogenic
RS2125314883 Health Risk Likely pathogenic Glaucoma 3A, Glaucoma 3, primary infantile
RS2125316074 Health Risk Likely pathogenic Glaucoma 3A, Primary congenital glaucoma, CYP1B1-related glaucoma with or without anterior segment dysgenesis
RS2465878985 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Glaucoma 3A, Anterior segment dysgenesis 6
RS2465879013 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
RS2465879029 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
RS2465882881 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
RS2465882986 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
RS2465883314 Health Risk Likely pathogenic
RS2465883438 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
RS2465883561 Health Risk Likely pathogenic Anterior segment dysgenesis, Anterior segment dysgenesis
RS2465883734 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
RS2465884101 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
RS2465884590 Health Risk Likely pathogenic Anterior segment dysgenesis 6, Anterior segment dysgenesis 6
1 2 3 Next »
Sign Up to Analyze Your DNA Log In