COG1 Chromosome 17

Component of oligomeric golgi complex 1
39 variants 39 Health Risk

Upload your DNA to see your personal genotypes for variants in COG1.

What This Gene Does
The protein encoded by this gene is one of eight proteins (Cog1-8) which form a Golgi-localized complex (COG) required for normal Golgi morphology and function. It is thought that this protein is required for steps in the normal medial and trans Golgi-associated processing of glycoconjugates and plays a role in the organization of the Golgi-localized complex. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Components of oligomeric golgi complex
Locus Type
gene with protein product
Location
17q25.1
Ensembl
ENSG00000166685
Associated Conditions (4)
COG1 congenital disorder of glycosylation
COG1-related disorder
Inborn genetic diseases
Nephrotic syndrome
Key Variants
RS117208167
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, COG1-related disorder, COG1 congenital disorder of glycosylation
Health Risk
RS1197833925
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, Inborn genetic diseases, COG1 congenital disorder of glycosylation
Health Risk
RS1229193421
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, Inborn genetic diseases, COG1 congenital disorder of glycosylation
Health Risk
RS141750466
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, COG1-related disorder, COG1 congenital disorder of glycosylation
Health Risk
RS142827255
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
Health Risk
RS144115463
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
Health Risk
RS146046236
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
Health Risk
RS146066919
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, COG1-related disorder, Inborn genetic diseases
Health Risk
RS147598221
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
Health Risk
RS148502827
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
Health Risk
RS149888309
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
Health Risk
RS185592690
Conflicting classifications of pathogenicity
COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
Health Risk
All Variants (39)
RSID Category Clinical Significance Conditions
RS117208167 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1-related disorder, COG1 congenital disorder of glycosylation
RS1197833925 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, Inborn genetic diseases, COG1 congenital disorder of glycosylation
RS1229193421 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, Inborn genetic diseases, COG1 congenital disorder of glycosylation
RS141750466 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1-related disorder, COG1 congenital disorder of glycosylation
RS142827255 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS144115463 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS146046236 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS146066919 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1-related disorder, Inborn genetic diseases
RS147598221 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS148502827 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS149888309 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS185592690 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS188853520 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS200144944 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS201123101 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS201263432 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS201364732 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS201867802 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS534708439 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, Inborn genetic diseases, COG1 congenital disorder of glycosylation
RS748732950 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1-related disorder, COG1 congenital disorder of glycosylation
RS759050295 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, Inborn genetic diseases, COG1 congenital disorder of glycosylation
RS766457949 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, Inborn genetic diseases, COG1 congenital disorder of glycosylation
RS769310036 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, Inborn genetic diseases, COG1 congenital disorder of glycosylation
RS772385793 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, Inborn genetic diseases, COG1 congenital disorder of glycosylation
RS774356907 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, Inborn genetic diseases, COG1 congenital disorder of glycosylation
RS781686684 Health Risk Conflicting classifications of pathogenicity COG1 congenital disorder of glycosylation, COG1-related disorder, COG1 congenital disorder of glycosylation
RS1555725221 Health Risk Likely pathogenic
RS1555725363 Health Risk Likely pathogenic
RS771513054 Health Risk Likely pathogenic COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS1568296260 Health Risk Pathogenic COG1 congenital disorder of glycosylation, Nephrotic syndrome, COG1 congenital disorder of glycosylation
RS1568298983 Health Risk Pathogenic COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS2061310130 Health Risk Pathogenic COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS2061375797 Health Risk Pathogenic COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS2145097019 Health Risk Pathogenic COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS2511081455 Health Risk Pathogenic COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS758521897 Health Risk Pathogenic COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS773341615 Health Risk Pathogenic COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS1227032564 Health Risk Pathogenic/Likely pathogenic COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
RS747606976 Health Risk Pathogenic/Likely pathogenic COG1 congenital disorder of glycosylation, COG1 congenital disorder of glycosylation
Sign Up to Analyze Your DNA Log In