CNKSR2 Chromosome X

Connector enhancer of kinase suppressor of Ras 2
40 variants 40 Health Risk

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What This Gene Does
This gene encodes a multidomain protein that functions as a scaffold protein to mediate the mitogen-activated protein kinase pathways downstream from Ras. This gene product is induced by vitamin D and inhibits apoptosis in certain cancer cells. It may also play a role in ternary complex assembly of synaptic proteins at the postsynaptic membrane and coupling of signal transduction to membrane/cytoskeletal remodeling. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Dec 2009]
Gene Info
Gene Group
"Pleckstrin homology domain containing|Sterile alpha motif domain containing|PDZ domain containing"
Locus Type
gene with protein product
Location
Xp22.12
Ensembl
ENSG00000149970
Associated Conditions (8)
Uterine corpus endometrial carcinoma
Intellectual disability
Inborn genetic diseases
X-linked
syndromic
Houge type
X-linked recessive seizure and neurodevelopmental deficit
Neurodevelopmental disorder
Key Variants
All Variants (40)
RSID Category Clinical Significance Conditions
RS113091231 Health Risk Conflicting classifications of pathogenicity Uterine corpus endometrial carcinoma, Uterine corpus endometrial carcinoma
RS144451192 Health Risk Conflicting classifications of pathogenicity Intellectual disability, Inborn genetic diseases, Intellectual disability
RS200533315 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS2147346551 Health Risk Conflicting classifications of pathogenicity Intellectual disability, X-linked, syndromic
RS757776373 Health Risk Conflicting classifications of pathogenicity
RS760890681 Health Risk Conflicting classifications of pathogenicity
RS1555941759 Health Risk Likely pathogenic X-linked recessive seizure and neurodevelopmental deficit, X-linked recessive seizure and neurodevelopmental deficit
RS1569161831 Health Risk Likely pathogenic Intellectual disability, Intellectual disability
RS1569272271 Health Risk Likely pathogenic Neurodevelopmental disorder, Neurodevelopmental disorder
RS1601952572 Health Risk Likely pathogenic
RS2092414327 Health Risk Likely pathogenic Intellectual disability, X-linked, syndromic
RS2147191275 Health Risk Likely pathogenic Intellectual disability, X-linked, syndromic
RS2519083192 Health Risk Likely pathogenic Intellectual disability, X-linked, syndromic
RS2519299753 Health Risk Likely pathogenic Intellectual disability, X-linked, syndromic
RS1064793729 Health Risk Pathogenic
RS1064794022 Health Risk Pathogenic
RS1569261319 Health Risk Pathogenic Intellectual disability, X-linked, syndromic
RS1602013845 Health Risk Pathogenic Intellectual disability, X-linked, syndromic
RS2090650922 Health Risk Pathogenic
RS2091890720 Health Risk Pathogenic
RS2092480152 Health Risk Pathogenic Intellectual disability, Intellectual disability
RS2092480172 Health Risk Pathogenic Intellectual disability, X-linked, syndromic
RS2147096420 Health Risk Pathogenic
RS2147123782 Health Risk Pathogenic Intellectual disability, X-linked, syndromic
RS2147123908 Health Risk Pathogenic
RS2147143428 Health Risk Pathogenic Intellectual disability, X-linked, syndromic
RS2147249014 Health Risk Pathogenic
RS2147250007 Health Risk Pathogenic
RS2147258522 Health Risk Pathogenic
RS2147268813 Health Risk Pathogenic Intellectual disability, X-linked, syndromic
RS2147283343 Health Risk Pathogenic Intellectual disability, X-linked, syndromic
RS2147283407 Health Risk Pathogenic
RS2519317743 Health Risk Pathogenic
RS2519358649 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS606231282 Health Risk Pathogenic Intellectual disability, X-linked, syndromic
RS886041712 Health Risk Pathogenic
RS886041798 Health Risk Pathogenic
RS904072058 Health Risk Pathogenic Intellectual disability, X-linked, syndromic
RS2519101342 Health Risk Pathogenic/Likely pathogenic Intellectual disability, X-linked, syndromic
RS2519358174 Health Risk Pathogenic/Likely pathogenic Intellectual disability, X-linked, syndromic
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