CHD3 Chromosome 17

Chromodomain helicase DNA binding protein 3
101 variants 101 Health Risk

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What This Gene Does
This gene encodes a member of the CHD family of proteins which are characterized by the presence of chromo (chromatin organization modifier) domains and SNF2-related helicase/ATPase domains. This protein is one of the components of a histone deacetylase complex referred to as the Mi-2/NuRD complex which participates in the remodeling of chromatin by deacetylating histones. Chromatin remodeling is essential for many processes including transcription. Autoantibodies against this protein are found in a subset of patients with dermatomyositis. Three alternatively spliced transcripts encoding different isoforms have been described. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
"PHD finger proteins|SNF2 related family|NuRD complex subunits|Small nucleolar RNA protein coding host genes"
Locus Type
gene with protein product
Location
17p13.1
Ensembl
ENSG00000170004
Associated Conditions (13)
Inborn genetic diseases
Snijders Blok-Campeau syndrome
CHD3-related disorder
Intellectual disability
Malignant tumor of esophagus
Lung cancer
Autism spectrum disorder
Congenital ocular coloboma
Neurodevelopmental abnormality
Melanoma
Global developmental delay
Cervical cancer
Marfanoid habitus and intellectual disability
Key Variants
RS1162732075
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS1248531611
Conflicting classifications of pathogenicity
Inborn genetic diseases, Snijders Blok-Campeau syndrome, Inborn genetic diseases
Health Risk
RS1350258866
Conflicting classifications of pathogenicity
Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
Health Risk
RS1394994913
Conflicting classifications of pathogenicity
Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
Health Risk
RS140448992
Conflicting classifications of pathogenicity
CHD3-related disorder, Snijders Blok-Campeau syndrome, Inborn genetic diseases
Health Risk
RS147796138
Conflicting classifications of pathogenicity
Inborn genetic diseases, CHD3-related disorder, Snijders Blok-Campeau syndrome
Health Risk
RS1555611692
Conflicting classifications of pathogenicity
Snijders Blok-Campeau syndrome, Inborn genetic diseases, Snijders Blok-Campeau syndrome
Health Risk
RS1567861571
Conflicting classifications of pathogenicity
Intellectual disability, Snijders Blok-Campeau syndrome, Intellectual disability
Health Risk
RS1970877175
Conflicting classifications of pathogenicity
Snijders Blok-Campeau syndrome, CHD3-related disorder, Snijders Blok-Campeau syndrome
Health Risk
RS200434912
Conflicting classifications of pathogenicity
Snijders Blok-Campeau syndrome, CHD3-related disorder, Malignant tumor of esophagus
Health Risk
RS2151569587
Conflicting classifications of pathogenicity
Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
Health Risk
RS2151603656
Conflicting classifications of pathogenicity
Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
Health Risk
All Variants (101)
RSID Category Clinical Significance Conditions
RS1162732075 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1248531611 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Snijders Blok-Campeau syndrome, Inborn genetic diseases
RS1350258866 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS1394994913 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS140448992 Health Risk Conflicting classifications of pathogenicity CHD3-related disorder, Snijders Blok-Campeau syndrome, Inborn genetic diseases
RS147796138 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, CHD3-related disorder, Snijders Blok-Campeau syndrome
RS1555611692 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Inborn genetic diseases, Snijders Blok-Campeau syndrome
RS1567861571 Health Risk Conflicting classifications of pathogenicity Intellectual disability, Snijders Blok-Campeau syndrome, Intellectual disability
RS1970877175 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, CHD3-related disorder, Snijders Blok-Campeau syndrome
RS200434912 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, CHD3-related disorder, Malignant tumor of esophagus
RS2151569587 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS2151603656 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS2151615708 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS2544705900 Health Risk Conflicting classifications of pathogenicity Autism spectrum disorder, CHD3-related disorder, Autism spectrum disorder
RS2544958607 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS2545018697 Health Risk Conflicting classifications of pathogenicity CHD3-related disorder, CHD3-related disorder
RS2545018939 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS2545018983 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS2545030956 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS372395250 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, CHD3-related disorder, Inborn genetic diseases
RS375492899 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Inborn genetic diseases, Snijders Blok-Campeau syndrome
RS550038952 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS61753146 Health Risk Conflicting classifications of pathogenicity CHD3-related disorder, CHD3-related disorder
RS755801203 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS780573521 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Congenital ocular coloboma, Inborn genetic diseases
RS967826828 Health Risk Conflicting classifications of pathogenicity Snijders Blok-Campeau syndrome, Inborn genetic diseases, CHD3-related disorder
RS1230899870 Health Risk Likely pathogenic Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS1314577386 Health Risk Likely pathogenic Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS1476775959 Health Risk Likely pathogenic
RS1482536453 Health Risk Likely pathogenic Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS1555612691 Health Risk Likely pathogenic
RS1567844992 Health Risk Likely pathogenic Intellectual disability, Intellectual disability
RS1567855081 Health Risk Likely pathogenic Intellectual disability, Snijders Blok-Campeau syndrome, Neurodevelopmental abnormality
RS1567855704 Health Risk Likely pathogenic Intellectual disability, Snijders Blok-Campeau syndrome, Intellectual disability
RS1567856045 Health Risk Likely pathogenic Intellectual disability, Snijders Blok-Campeau syndrome, Intellectual disability
RS1567856331 Health Risk Likely pathogenic Intellectual disability, Snijders Blok-Campeau syndrome, Inborn genetic diseases
RS1567860075 Health Risk Likely pathogenic Intellectual disability, Snijders Blok-Campeau syndrome, Intellectual disability
RS1567860640 Health Risk Likely pathogenic Snijders Blok-Campeau syndrome, Intellectual disability, Snijders Blok-Campeau syndrome
RS1567860919 Health Risk Likely pathogenic Intellectual disability, Snijders Blok-Campeau syndrome, Intellectual disability
RS1567861489 Health Risk Likely pathogenic Intellectual disability, Snijders Blok-Campeau syndrome, Intellectual disability
RS1567861894 Health Risk Likely pathogenic Intellectual disability, Snijders Blok-Campeau syndrome, Intellectual disability
RS1567864750 Health Risk Likely pathogenic Intellectual disability, Snijders Blok-Campeau syndrome, Intellectual disability
RS1567877108 Health Risk Likely pathogenic Intellectual disability, Snijders Blok-Campeau syndrome, Intellectual disability
RS1567878511 Health Risk Likely pathogenic Intellectual disability, Intellectual disability
RS1970460175 Health Risk Likely pathogenic Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS1970542838 Health Risk Likely pathogenic
RS1970772602 Health Risk Likely pathogenic Inborn genetic diseases, Inborn genetic diseases, Melanoma
RS2151542224 Health Risk Likely pathogenic Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
RS2151561113 Health Risk Likely pathogenic
RS2151573039 Health Risk Likely pathogenic Snijders Blok-Campeau syndrome, Snijders Blok-Campeau syndrome
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