CHAT Chromosome 10

Choline O-acetyltransferase
128 variants 128 Health Risk

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What This Gene Does
This gene encodes an enzyme which catalyzes the biosynthesis of the neurotransmitter acetylcholine. This gene product is a characteristic feature of cholinergic neurons, and changes in these neurons may explain some of the symptoms of Alzheimer's disease. Polymorphisms in this gene have been associated with Alzheimer's disease and mild cognitive impairment. Mutations in this gene are associated with congenital myasthenic syndrome associated with episodic apnea. Multiple transcript variants encoding different isoforms have been found for this gene, and some of these variants have been shown to encode more than one isoform. [provided by RefSeq, May 2010]
Gene Info
Gene Group
Choline/carnitine acyltransferase family
Locus Type
gene with protein product
Location
10q11.23
Ensembl
ENSG00000070748
Associated Conditions (7)
Familial infantile myasthenia
Inborn genetic diseases
Congenital myasthenic syndrome
CHAT-related disorder
11 conditions
Abnormality of the musculature
Congenital myasthenic syndrome 4C
Key Variants
RS114545628
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Familial infantile myasthenia
Health Risk
RS114719193
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Familial infantile myasthenia
Health Risk
RS115877658
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
Health Risk
RS116071049
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Familial infantile myasthenia
Health Risk
RS1198717023
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Familial infantile myasthenia
Health Risk
RS1384661323
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Familial infantile myasthenia
Health Risk
RS141127966
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
Health Risk
RS142285373
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
Health Risk
RS143723043
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Familial infantile myasthenia
Health Risk
RS147815999
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Familial infantile myasthenia
Health Risk
RS148155075
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
Health Risk
RS148525631
Conflicting classifications of pathogenicity
Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
Health Risk
All Variants (128)
RSID Category Clinical Significance Conditions
RS114545628 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS114719193 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS115877658 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS116071049 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS1198717023 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS1384661323 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS141127966 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS142285373 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS143723043 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS147815999 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS148155075 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS148525631 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS199926163 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS200176236 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS200423662 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS201479289 Health Risk Conflicting classifications of pathogenicity Congenital myasthenic syndrome, Familial infantile myasthenia, Congenital myasthenic syndrome
RS201616704 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS202059535 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS2496288024 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS372298555 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS376641216 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, CHAT-related disorder
RS376994468 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, CHAT-related disorder, Familial infantile myasthenia
RS531450737 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS538478136 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS542610160 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS547073881 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS551219437 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia, Familial infantile myasthenia
RS55702495 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS560648873 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS574542737 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS61731735 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS750942168 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS75262191 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS755783618 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS757733319 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS759310217 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS76570508 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS776411377 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS777336258 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS779668516 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Familial infantile myasthenia
RS79414242 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, CHAT-related disorder, Familial infantile myasthenia
RS8178989 Health Risk Conflicting classifications of pathogenicity Familial infantile myasthenia, Inborn genetic diseases, Familial infantile myasthenia
RS1207292931 Health Risk Likely pathogenic Familial infantile myasthenia, Familial infantile myasthenia
RS121912817 Health Risk Likely pathogenic Familial infantile myasthenia, Familial infantile myasthenia
RS121912818 Health Risk Likely pathogenic Familial infantile myasthenia, Familial infantile myasthenia
RS121912821 Health Risk Likely pathogenic Familial infantile myasthenia, Congenital myasthenic syndrome, Familial infantile myasthenia
RS121912822 Health Risk Likely pathogenic Familial infantile myasthenia, Congenital myasthenic syndrome, Familial infantile myasthenia
RS1272947184 Health Risk Likely pathogenic Familial infantile myasthenia, Familial infantile myasthenia
RS1306112783 Health Risk Likely pathogenic Familial infantile myasthenia, Congenital myasthenic syndrome, Familial infantile myasthenia
RS1325924035 Health Risk Likely pathogenic Familial infantile myasthenia, Familial infantile myasthenia
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