CEP83 Chromosome 12

Centrosomal protein 83
49 variants 49 Health Risk

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What This Gene Does
The protein encoded by this gene is a centriolar protein involved in primary cilium assembly. Defects in this gene have been associated with infantile nephronophthisis and intellectual disability. [provided by RefSeq, Oct 2016]
Associated Conditions (5)
Nephronophthisis 18
CEP83-related disorder
Inborn genetic diseases
Ciliopathy
Nephronophthisis
Key Variants
All Variants (49)
RSID Category Clinical Significance Conditions
RS1370476857 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Nephronophthisis 18
RS150415429 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, CEP83-related disorder, Nephronophthisis 18
RS181264654 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Nephronophthisis 18
RS199617764 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Inborn genetic diseases, CEP83-related disorder
RS199871798 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Inborn genetic diseases, Nephronophthisis 18
RS200232390 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Inborn genetic diseases, Nephronophthisis 18
RS200971081 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Ciliopathy, Nephronophthisis 18
RS562683007 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Nephronophthisis 18
RS577668407 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Inborn genetic diseases, Nephronophthisis 18
RS748658606 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Inborn genetic diseases, Nephronophthisis 18
RS757301110 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Nephronophthisis 18
RS765908199 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Nephronophthisis 18
RS906852829 Health Risk Conflicting classifications of pathogenicity Nephronophthisis 18, Nephronophthisis 18
RS1555237944 Health Risk Likely pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2541088913 Health Risk Likely pathogenic
RS2541287399 Health Risk Likely pathogenic Ciliopathy, Ciliopathy
RS763352069 Health Risk Likely pathogenic
RS1064794347 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS1162641847 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS1187876547 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS1198459012 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS1207804224 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS1216945458 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS1276979881 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS1437433749 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2061111812 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2061113374 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2063356920 Health Risk Pathogenic
RS2136488957 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2136514301 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2136515432 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2137174483 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2137575733 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2541064312 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2541088599 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2541287551 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS2541678147 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS368619022 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS587777486 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS587777487 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS587777488 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS750092874 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS763560797 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS777412559 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS780500128 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis, Nephronophthisis 18
RS879255575 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS879255576 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS922686745 Health Risk Pathogenic Nephronophthisis 18, Nephronophthisis 18
RS369483167 Health Risk Pathogenic/Likely pathogenic Nephronophthisis 18, Nephronophthisis 18
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