BUB1B Chromosome 15

BUB1 mitotic checkpoint serine/threonine kinase B
102 variants 102 Health Risk

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What This Gene Does
This gene encodes a kinase involved in spindle checkpoint function. The protein has been localized to the kinetochore and plays a role in the inhibition of the anaphase-promoting complex/cyclosome (APC/C), delaying the onset of anaphase and ensuring proper chromosome segregation. Impaired spindle checkpoint function has been found in many forms of cancer. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
BUB1 mitotic checkpoint serine/threonine kinase family
Locus Type
gene with protein product
Location
15q15.1
Ensembl
ENSG00000156970
Associated Conditions (10)
Mosaic variegated aneuploidy syndrome 1
Inborn genetic diseases
See cases
Colorectal cancer
BUB1B-related disorder
Premature chromatid separation trait
Carcinoma of colon
Mosaic variegated aneuploidy syndrome
Microcephaly
Ovarian cancer
Key Variants
RS117485407
Conflicting classifications of pathogenicity
Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
Health Risk
RS1221831901
Conflicting classifications of pathogenicity
Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
Health Risk
RS1326535455
Conflicting classifications of pathogenicity
Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases
Health Risk
RS141013408
Conflicting classifications of pathogenicity
Mosaic variegated aneuploidy syndrome 1, See cases, Inborn genetic diseases
Health Risk
RS141953425
Conflicting classifications of pathogenicity
Mosaic variegated aneuploidy syndrome 1, Carcinoma of colon, Premature chromatid separation trait
Health Risk
RS1422532977
Conflicting classifications of pathogenicity
Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
Health Risk
RS143232848
Conflicting classifications of pathogenicity
Mosaic variegated aneuploidy syndrome 1, Microcephaly, Inborn genetic diseases
Health Risk
RS1440328650
Conflicting classifications of pathogenicity
Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
Health Risk
RS145184714
Conflicting classifications of pathogenicity
Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
Health Risk
RS148159407
Conflicting classifications of pathogenicity
Carcinoma of colon, Premature chromatid separation trait, Mosaic variegated aneuploidy syndrome 1
Health Risk
RS150707631
Conflicting classifications of pathogenicity
Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
Health Risk
RS1595518738
Conflicting classifications of pathogenicity
Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
Health Risk
All Variants (102)
RSID Category Clinical Significance Conditions
RS117485407 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS1221831901 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS1326535455 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases
RS141013408 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, See cases, Inborn genetic diseases
RS141953425 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Carcinoma of colon, Premature chromatid separation trait
RS1422532977 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS143232848 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Microcephaly, Inborn genetic diseases
RS1440328650 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS145184714 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS148159407 Health Risk Conflicting classifications of pathogenicity Carcinoma of colon, Premature chromatid separation trait, Mosaic variegated aneuploidy syndrome 1
RS150707631 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS1595518738 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS201251790 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, BUB1B-related disorder, Mosaic variegated aneuploidy syndrome 1
RS201927813 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS2037686992 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases
RS2140911352 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS2542556120 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases
RS2542571638 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS28989182 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Premature chromatid separation trait, Mosaic variegated aneuploidy syndrome 1
RS28989183 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Premature chromatid separation trait, Inborn genetic diseases
RS34700927 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, BUB1B-related disorder, Mosaic variegated aneuploidy syndrome 1
RS368585401 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS368869250 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases
RS373105304 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS375798678 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Colorectal cancer
RS556193159 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS557521971 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Ovarian cancer, Inborn genetic diseases
RS746933398 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS751421137 Health Risk Conflicting classifications of pathogenicity Premature chromatid separation trait, Mosaic variegated aneuploidy syndrome 1, Colorectal cancer
RS759232092 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS763676435 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS770219125 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS770579508 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS772218663 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS772525026 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1
RS774654439 Health Risk Conflicting classifications of pathogenicity Mosaic variegated aneuploidy syndrome 1, Ovarian cancer, Mosaic variegated aneuploidy syndrome 1
RS777880062 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Mosaic variegated aneuploidy syndrome 1, Inborn genetic diseases
RS896037493 Health Risk Conflicting classifications of pathogenicity Ovarian cancer, Inborn genetic diseases, Ovarian cancer
RS971891189 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Ovarian cancer, Mosaic variegated aneuploidy syndrome 1
RS1290506364 Health Risk Likely pathogenic Mosaic variegated aneuploidy syndrome, Mosaic variegated aneuploidy syndrome
RS1309303130 Health Risk Likely pathogenic
RS147160147 Health Risk Likely pathogenic Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS1566830754 Health Risk Likely pathogenic Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS2037226022 Health Risk Likely pathogenic Premature chromatid separation trait, Premature chromatid separation trait
RS2037228249 Health Risk Likely pathogenic Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS2037350060 Health Risk Likely pathogenic Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS2037726277 Health Risk Likely pathogenic Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS2542508482 Health Risk Likely pathogenic Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS2542554942 Health Risk Likely pathogenic Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
RS2542555071 Health Risk Likely pathogenic Mosaic variegated aneuploidy syndrome 1, Mosaic variegated aneuploidy syndrome 1
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