BRIP1 Chromosome 17

BRCA1 interacting DNA helicase 1
1091 variants 1091 Health Risk

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What This Gene Does
The protein encoded by this gene is a member of the RecQ DEAH helicase family and interacts with the BRCT repeats of breast cancer, type 1 (BRCA1). The bound complex is important in the normal double-strand break repair function of breast cancer, type 1 (BRCA1). This gene may be a target of germline cancer-inducing mutations. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
"DEAH-box helicases|FA complementation groups|BRCA1 B complex"
Locus Type
gene with protein product
Location
17q23.2
Ensembl
ENSG00000136492
Associated Conditions (41)
Familial cancer of breast
Fanconi anemia complementation group J
Hereditary cancer-predisposing syndrome
Breast and/or ovarian cancer
Familial ovarian cancer
BRIP1-related disorder
Hereditary breast ovarian cancer syndrome
Ovarian cancer
Gastric cancer
Malignant tumor of breast
Diffuse intrinsic pontine glioma
Breast carcinoma
Inherited ovarian cancer (without breast cancer)
Breast-ovarian cancer
familial
susceptibility to
2
Breast cancer
early-onset
Monogenic short stature
+21 more conditions
Key Variants
RS1003917080
Conflicting classifications of pathogenicity
Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
Health Risk
RS1008150951
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
Health Risk
RS1034545913
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Fanconi anemia complementation group J, Familial cancer of breast
Health Risk
RS1034551306
Conflicting classifications of pathogenicity
Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
Health Risk
RS1046992728
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
Health Risk
RS1057517647
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
Health Risk
RS1057521675
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
Health Risk
RS1057523068
Conflicting classifications of pathogenicity
Fanconi anemia complementation group J, Familial cancer of breast, Hereditary cancer-predisposing syndrome
Health Risk
RS1060501738
Conflicting classifications of pathogenicity
Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
Health Risk
RS1060501740
Conflicting classifications of pathogenicity
Familial cancer of breast, Fanconi anemia complementation group J, Familial cancer of breast
Health Risk
RS1060501774
Conflicting classifications of pathogenicity
Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
Health Risk
RS1060501781
Conflicting classifications of pathogenicity
Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
Health Risk
All Variants (1091)
RSID Category Clinical Significance Conditions
RS1442433909 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Hereditary cancer-predisposing syndrome
RS145601931 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1457869893 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS145855459 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Fanconi anemia complementation group J, Familial cancer of breast
RS145859791 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS147119272 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS1475317357 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS1479296707 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Hereditary cancer-predisposing syndrome
RS1484234707 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS148429663 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS148752066 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Fanconi anemia complementation group J, Familial cancer of breast
RS149364097 Health Risk Conflicting classifications of pathogenicity Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome, Familial cancer of breast
RS149529390 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS150313156 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS150444311 Health Risk Conflicting classifications of pathogenicity Fanconi anemia complementation group J, Familial cancer of breast, Fanconi anemia complementation group J
RS150624408 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS150813402 Health Risk Conflicting classifications of pathogenicity Fanconi anemia complementation group J, Familial cancer of breast, Hereditary cancer-predisposing syndrome
RS1555572672 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555572908 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555572999 Health Risk Conflicting classifications of pathogenicity Fanconi anemia complementation group J, Familial cancer of breast, Hereditary cancer-predisposing syndrome
RS1555573247 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555573412 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS1555574710 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Familial cancer of breast
RS1555574711 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555574712 Health Risk Conflicting classifications of pathogenicity Fanconi anemia complementation group J, Familial cancer of breast, Hereditary cancer-predisposing syndrome
RS1555574772 Health Risk Conflicting classifications of pathogenicity Fanconi anemia complementation group J, Familial cancer of breast, Hereditary cancer-predisposing syndrome
RS1555590464 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS1555591351 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555602149 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555602537 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555603597 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS1555603645 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555605906 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555605965 Health Risk Conflicting classifications of pathogenicity Fanconi anemia complementation group J, Familial cancer of breast, Fanconi anemia complementation group J
RS1555607035 Health Risk Conflicting classifications of pathogenicity Fanconi anemia complementation group J, Familial cancer of breast, Hereditary cancer-predisposing syndrome
RS1555607195 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS1555607258 Health Risk Conflicting classifications of pathogenicity Breast cancer, early-onset, Hereditary cancer-predisposing syndrome
RS1555607674 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Fanconi anemia complementation group J, Familial cancer of breast
RS1555607763 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555615717 Health Risk Conflicting classifications of pathogenicity Fanconi anemia complementation group J, Familial cancer of breast, Hereditary cancer-predisposing syndrome
RS1555616229 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS1555617897 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555617934 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1555618360 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Fanconi anemia complementation group J, Familial cancer of breast
RS1567727060 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Hereditary cancer-predisposing syndrome
RS1567727439 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS1567728557 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Fanconi anemia complementation group J, Familial cancer of breast
RS1567728809 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Familial cancer of breast, Fanconi anemia complementation group J
RS1567731308 Health Risk Conflicting classifications of pathogenicity Familial cancer of breast, Fanconi anemia complementation group J, Hereditary cancer-predisposing syndrome
RS1567755628 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Ovarian cancer, Fanconi anemia complementation group J
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