ALG1 Chromosome 16

ALG1 chitobiosyldiphosphodolichol beta-mannosyltransferase
128 variants 128 Health Risk

Upload your DNA to see your personal genotypes for variants in ALG1.

What This Gene Does
The enzyme encoded by this gene catalyzes the first mannosylation step in the biosynthesis of lipid-linked oligosaccharides. This gene is mutated in congenital disorder of glycosylation type Ik. [provided by RefSeq, Dec 2008]
Gene Info
Gene Group
Glycosyl transferases group 1 domain containing
Locus Type
gene with protein product
Location
16p13.3
Ensembl
ENSG00000033011
Associated Conditions (8)
ALG1-congenital disorder of glycosylation
Congenital disorder of glycosylation
Inborn genetic diseases
ALG1-related disorder
Finnish congenital nephrotic syndrome
Encephalopathy
ALG12-congenital disorder of glycosylation
Congenital disorder of glycosylation type I
Key Variants
RS1057520122
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, Congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
Health Risk
RS1261895166
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
Health Risk
RS1373315673
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, Inborn genetic diseases, ALG1-congenital disorder of glycosylation
Health Risk
RS1436106795
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
Health Risk
RS143676440
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
Health Risk
RS145158686
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
Health Risk
RS145317306
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, Inborn genetic diseases, ALG1-related disorder
Health Risk
RS147412842
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, ALG1-related disorder, Inborn genetic diseases
Health Risk
RS148611855
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
Health Risk
RS148933850
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, Inborn genetic diseases, ALG1-congenital disorder of glycosylation
Health Risk
RS150272167
Conflicting classifications of pathogenicity
ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
Health Risk
RS1596259672
Conflicting classifications of pathogenicity
Congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation, Congenital disorder of glycosylation
Health Risk
All Variants (128)
RSID Category Clinical Significance Conditions
RS2505868653 Health Risk Pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS375670899 Health Risk Pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS387906927 Health Risk Pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS752922461 Health Risk Pathogenic Congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation, Congenital disorder of glycosylation
RS753904901 Health Risk Pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS756236917 Health Risk Pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS757512219 Health Risk Pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS758259853 Health Risk Pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS771153009 Health Risk Pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS776264264 Health Risk Pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS889550402 Health Risk Pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS1372794201 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS1474783444 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS151173406 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, Congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS1596261268 Health Risk Pathogenic/Likely pathogenic Congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation, Congenital disorder of glycosylation
RS1957009416 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS267606651 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, Inborn genetic diseases, ALG1-congenital disorder of glycosylation
RS28939378 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, Inborn genetic diseases, Congenital disorder of glycosylation
RS369160589 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, Congenital disorder of glycosylation, Encephalopathy
RS374928784 Health Risk Pathogenic/Likely pathogenic Congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation, Congenital disorder of glycosylation
RS398124348 Health Risk Pathogenic/Likely pathogenic Inborn genetic diseases, Congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS553396382 Health Risk Pathogenic/Likely pathogenic Congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation, Congenital disorder of glycosylation
RS746019074 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, Congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS750451819 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS763496595 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS776990436 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, ALG1-related disorder, ALG1-congenital disorder of glycosylation
RS780107088 Health Risk Pathogenic/Likely pathogenic ALG1-congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation
RS794727073 Health Risk Pathogenic/Likely pathogenic Congenital disorder of glycosylation, ALG1-congenital disorder of glycosylation, Congenital disorder of glycosylation
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