ALDH3A2 Chromosome 17

Aldehyde dehydrogenase 3 family member A2
176 variants 176 Health Risk

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What This Gene Does
Aldehyde dehydrogenase isozymes are thought to play a major role in the detoxification of aldehydes generated by alcohol metabolism and lipid peroxidation. This gene product catalyzes the oxidation of long-chain aliphatic aldehydes to fatty acid. Mutations in the gene cause Sjogren-Larsson syndrome. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Aldehyde dehydrogenases
Locus Type
gene with protein product
Location
17p11.2
Ensembl
ENSG00000072210
Associated Conditions (7)
Sjögren-Larsson syndrome
Inborn genetic diseases
ALDH3A2-related disorder
Familial cancer of breast
Gastric cancer
Cerebral palsy
Malignant tumor of esophagus
Key Variants
RS1010078101
Conflicting classifications of pathogenicity
Health Risk
RS1054840414
Conflicting classifications of pathogenicity
Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
Health Risk
RS1320588121
Conflicting classifications of pathogenicity
Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
Health Risk
RS140649688
Conflicting classifications of pathogenicity
Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
Health Risk
RS141112437
Conflicting classifications of pathogenicity
Inborn genetic diseases, Sjögren-Larsson syndrome, Inborn genetic diseases
Health Risk
RS143717984
Conflicting classifications of pathogenicity
Sjögren-Larsson syndrome, Inborn genetic diseases, Sjögren-Larsson syndrome
Health Risk
RS144496536
Conflicting classifications of pathogenicity
Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
Health Risk
RS147190807
Conflicting classifications of pathogenicity
Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
Health Risk
RS147200808
Conflicting classifications of pathogenicity
Sjögren-Larsson syndrome, Inborn genetic diseases, Sjögren-Larsson syndrome
Health Risk
RS148944691
Conflicting classifications of pathogenicity
Sjögren-Larsson syndrome, ALDH3A2-related disorder, Familial cancer of breast
Health Risk
RS150927045
Conflicting classifications of pathogenicity
Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
Health Risk
RS181889379
Conflicting classifications of pathogenicity
Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
Health Risk
All Variants (176)
RSID Category Clinical Significance Conditions
RS1010078101 Health Risk Conflicting classifications of pathogenicity
RS1054840414 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1320588121 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS140649688 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS141112437 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Sjögren-Larsson syndrome, Inborn genetic diseases
RS143717984 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Inborn genetic diseases, Sjögren-Larsson syndrome
RS144496536 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS147190807 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS147200808 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Inborn genetic diseases, Sjögren-Larsson syndrome
RS148944691 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, ALDH3A2-related disorder, Familial cancer of breast
RS150927045 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS181889379 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS192458322 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS199548781 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS370654268 Health Risk Conflicting classifications of pathogenicity
RS373251784 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS67939114 Health Risk Conflicting classifications of pathogenicity ALDH3A2-related disorder, Sjögren-Larsson syndrome, ALDH3A2-related disorder
RS72547554 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome, ALDH3A2-related disorder
RS746519259 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS749679693 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS752169967 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS756275242 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS770078722 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS773093556 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS886052688 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS886052689 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS886052690 Health Risk Conflicting classifications of pathogenicity Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1036733598 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1057516386 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1057516481 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1057516742 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1057516851 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1057516863 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1057517004 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1057517190 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1057517278 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1057517299 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS112346474 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1265969343 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1400349287 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1456560062 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS1555534430 Health Risk Likely pathogenic
RS1555534434 Health Risk Likely pathogenic
RS1555534472 Health Risk Likely pathogenic
RS1597556369 Health Risk Likely pathogenic
RS201985073 Health Risk Likely pathogenic
RS2152326727 Health Risk Likely pathogenic
RS2152328249 Health Risk Likely pathogenic
RS2152328724 Health Risk Likely pathogenic Sjögren-Larsson syndrome, Sjögren-Larsson syndrome
RS2152328756 Health Risk Likely pathogenic
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