ADCY5 Chromosome 3

Adenylate cyclase 5
95 variants 95 Health Risk

Upload your DNA to see your personal genotypes for variants in ADCY5.

What This Gene Does
This gene encodes a member of the membrane-bound adenylyl cyclase enzymes. Adenylyl cyclases mediate G protein-coupled receptor signaling through the synthesis of the second messenger cAMP. Activity of the encoded protein is stimulated by the Gs alpha subunit of G protein-coupled receptors and is inhibited by protein kinase A, calcium and Gi alpha subunits. Single nucleotide polymorphisms in this gene may be associated with low birth weight and type 2 diabetes. Alternatively spliced transcript variants that encode different isoforms have been observed for this gene. [provided by RefSeq, Dec 2010]
Gene Info
Gene Group
Adenylate cyclases
Locus Type
gene with protein product
Location
3q21.1
Ensembl
ENSG00000173175
Associated Conditions (10)
Inborn genetic diseases
ADCY5-related disorder
Dyskinesia with orofacial involvement
autosomal dominant
Morphological central nervous system abnormality
Hereditary ataxia
autosomal recessive
Neurodevelopmental disorder with hyperkinetic movements and dyskinesia
See cases
Neurodevelopmental delay
Key Variants
All Variants (95)
RSID Category Clinical Significance Conditions
RS921195392 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS988224463 Health Risk Conflicting classifications of pathogenicity Dyskinesia with orofacial involvement, autosomal dominant, autosomal recessive
RS1057520218 Health Risk Likely pathogenic
RS1085308027 Health Risk Likely pathogenic
RS1553718863 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS1553726054 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS1553751019 Health Risk Likely pathogenic ADCY5-related disorder, ADCY5-related disorder
RS1576526285 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS1576606182 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS1576606282 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS1576704514 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS1941427629 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS2107658867 Health Risk Likely pathogenic
RS2108269869 Health Risk Likely pathogenic
RS2108372289 Health Risk Likely pathogenic
RS2108390731 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal recessive, Dyskinesia with orofacial involvement
RS2472682698 Health Risk Likely pathogenic
RS2472872923 Health Risk Likely pathogenic
RS2472988765 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS765349480 Health Risk Likely pathogenic
RS781491004 Health Risk Likely pathogenic
RS864309483 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Inborn genetic diseases
RS910314734 Health Risk Likely pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS1007363034 Health Risk Pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS1215504032 Health Risk Pathogenic
RS1553718964 Health Risk Pathogenic
RS1553724606 Health Risk Pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS1553732126 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS1553751151 Health Risk Pathogenic
RS1553751262 Health Risk Pathogenic Inborn genetic diseases, Dyskinesia with orofacial involvement, autosomal recessive
RS2107658582 Health Risk Pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS2108148749 Health Risk Pathogenic Neurodevelopmental disorder with hyperkinetic movements and dyskinesia, Neurodevelopmental disorder with hyperkinetic movements and dyskinesia
RS2108372267 Health Risk Pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS2108384208 Health Risk Pathogenic Neurodevelopmental disorder with hyperkinetic movements and dyskinesia, Neurodevelopmental disorder with hyperkinetic movements and dyskinesia
RS2472863379 Health Risk Pathogenic
RS2473327728 Health Risk Pathogenic
RS756172692 Health Risk Pathogenic Neurodevelopmental disorder with hyperkinetic movements and dyskinesia, Neurodevelopmental disorder with hyperkinetic movements and dyskinesia
RS757156390 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS775132310 Health Risk Pathogenic
RS796065306 Health Risk Pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS797045002 Health Risk Pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS864309484 Health Risk Pathogenic Dyskinesia with orofacial involvement, autosomal dominant, Dyskinesia with orofacial involvement
RS864309515 Health Risk Pathogenic Dyskinesia with orofacial involvement, autosomal dominant, See cases
RS1365372289 Health Risk Pathogenic/Likely pathogenic Inborn genetic diseases, Dyskinesia with orofacial involvement, autosomal recessive
RS147646506 Health Risk Pathogenic/Likely pathogenic
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